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Total number of protein in "GO:0098798" GO term:  117

Identifier UniProt Gene UniProt Accession UniProt Name Chromosome GO term Database Cancer Driver Number of missense mutations Missense mutation per residues Number of disordered residues Number of mutations in disordered regions Disordered missense mutations per residues Number of OMIM mutation
AFG3L2 AFG3L2 Q9Y4W6 AFG3-like protein 2 chr18 GO:0098798 Not Cancer Driver No 72 0.09 162 10 0.062 22
AGK AGK Q53H12 Acylglycerol kinase, mitochondrial chr7 GO:0098798 Not Cancer Driver No 71 0.168 77 6 0.078 0
AP000311.1 AP000311.1 H7C0C1 ATP synthase subunit O, mitochondrial (Fragment) chr21 GO:0098798 Not Cancer Driver No 27 0.112 27 5 0.185 0
APOO APOO Q9BUR5 MICOS complex subunit MIC26 chrX GO:0098798 Not Cancer Driver No 25 0.126 23 4 0.174 0
APOOL APOOL Q6UXV4 MICOS complex subunit MIC27 chrX GO:0098798 Not Cancer Driver No 31 0.116 91 8 0.088 0
ATP5F1A_ENST00000282050 ATP5F1A P25705 ATP synthase subunit alpha, mitochondrial chr18 GO:0098798 Not Cancer Driver No 66 0.119 23 5 0.217 2
ATP5F1B ATP5F1B P06576 ATP synthase subunit beta, mitochondrial chr12 GO:0098798 Not Cancer Driver No 60 0.113 85 8 0.094 0
ATP5F1C ATP5F1C P36542 ATP synthase subunit gamma, mitochondrial chr10 GO:0098798 Not Cancer Driver No 39 0.131 11 0 0.0 0
ATP5F1D_ENST00000591660 ATP5F1D P30049 ATP synthase subunit delta, mitochondrial chr19 GO:0098798 Not Cancer Driver No 7 0.042 5 1 0.2 2
ATP5F1E_ENST00000395663 ATP5F1E P56381 ATP synthase subunit epsilon, mitochondrial chr20 GO:0098798 Not Cancer Driver No 3 0.059 1 0 0.0 1
ATP5PD ATP5PD O75947 ATP synthase subunit d, mitochondrial chr17 GO:0098798 Not Cancer Driver No 12 0.075 15 0 0.0 0
ATP5PO ATP5PO P48047 ATP synthase subunit O, mitochondrial chr21 GO:0098798 Not Cancer Driver No 19 0.089 9 2 0.222 0
BAX_ENST00000345358 BAX Q07812 Apoptosis regulator BAX chr19 GO:0098798 Census Yes 30 0.156 39 2 0.051 0
BCKDHA BCKDHA P12694 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial chr19 GO:0098798 Not Cancer Driver No 53 0.119 121 18 0.149 11
BCKDHB BCKDHB P21953 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial chr6 GO:0098798 Not Cancer Driver No 47 0.12 23 3 0.13 5
BCKDK BCKDK O14874 [3-methyl-2-oxobutanoate dehydrogenase [lipoamide]] kinase, mitochondrial chr16 GO:0098798 Not Cancer Driver No 62 0.15 39 3 0.077 3
C15orf48_ENST00000396650 NMES1 Q9C002 Normal mucosa of esophagus-specific gene 1 protein chr15 GO:0098798 Not Cancer Driver No 14 0.169 10 1 0.1 0
C19orf70_ENST00000309324 MICOS13 Q5XKP0 MICOS complex subunit MIC13 chr19 GO:0098798 Not Cancer Driver No 12 0.102 3 0 0.0 0
CHCHD10_ENST00000484558 CHCHD10 Q8WYQ3 Coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial chr22 GO:0098798 Not Cancer Driver No 8 0.056 97 4 0.041 4
CHCHD3 CHCHD3 Q9NX63 MICOS complex subunit MIC19 chr7 GO:0098798 Not Cancer Driver No 26 0.115 143 16 0.112 0
CHCHD6 CHCHD6 Q9BRQ6 MICOS complex subunit MIC25 chr3 GO:0098798 Not Cancer Driver No 27 0.115 194 24 0.124 0
CLPX CLPX O76031 ATP-dependent Clp protease ATP-binding subunit clpX-like, mitochondrial chr15 GO:0098798 Not Cancer Driver No 66 0.104 195 22 0.113 1
COX4I1 COX4I1 P13073 Cytochrome c oxidase subunit 4 isoform 1, mitochondrial chr16 GO:0098798 Not Cancer Driver No 17 0.101 5 1 0.2 1
COX4I2 COX4I2 Q96KJ9 Cytochrome c oxidase subunit 4 isoform 2, mitochondrial chr20 GO:0098798 Not Cancer Driver No 26 0.152 36 4 0.111 1
COX5A COX5A P20674 Cytochrome c oxidase subunit 5A, mitochondrial chr15 GO:0098798 Not Cancer Driver No 20 0.133 14 5 0.357 1
COX5B COX5B P10606 Cytochrome c oxidase subunit 5B, mitochondrial chr2 GO:0098798 Not Cancer Driver No 16 0.124 58 6 0.103 0
COX6A1 COX6A1 P12074 Cytochrome c oxidase subunit 6A1, mitochondrial chr12 GO:0098798 Not Cancer Driver No 17 0.156 48 5 0.104 0
COX6A2 COX6A2 Q02221 Cytochrome c oxidase subunit 6A2, mitochondrial chr16 GO:0098798 Not Cancer Driver No 14 0.144 42 8 0.19 2
COX6B1_ENST00000592141 COX6B1 P14854 Cytochrome c oxidase subunit 6B1 chr19 GO:0098798 Not Cancer Driver No 15 0.174 23 6 0.261 2
COX6C_ENST00000522940 COX6C P09669 Cytochrome c oxidase subunit 6C chr8 GO:0098798 Census Yes 14 0.187 0 0 0.0 0
COX7A1 COX7A1 P24310 Cytochrome c oxidase subunit 7A1, mitochondrial chr19 GO:0098798 Not Cancer Driver No 10 0.127 0 0 0.0 0
COX7A2L COX7A2L O14548 Cytochrome c oxidase subunit 7A-related protein, mitochondrial chr2 GO:0098798 Not Cancer Driver No 13 0.114 0 0 0.0 0
COX7B COX7B P24311 Cytochrome c oxidase subunit 7B, mitochondrial chrX GO:0098798 Not Cancer Driver No 19 0.237 28 7 0.25 0
COX7C COX7C P15954 Cytochrome c oxidase subunit 7C, mitochondrial chr5 GO:0098798 Not Cancer Driver No 7 0.111 0 0 0.0 0
COX8A COX8A P10176 Cytochrome c oxidase subunit 8A, mitochondrial chr11 GO:0098798 Not Cancer Driver No 10 0.145 1 0 0.0 0
COX8C COX8C Q7Z4L0 Cytochrome c oxidase subunit 8C, mitochondrial chr14 GO:0098798 Not Cancer Driver No 11 0.153 12 2 0.167 0
DBT DBT P11182 Lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial chr1 GO:0098798 Not Cancer Driver No 64 0.133 81 11 0.136 3
DLAT DLAT P10515 Dihydrolipoyllysine-residue acetyltransferase component of pyruvate dehydrogenase complex, mitochondrial chr11 GO:0098798 Not Cancer Driver No 63 0.097 294 42 0.143 0
DLD DLD P09622 Dihydrolipoyl dehydrogenase, mitochondrial chr7 GO:0098798 Not Cancer Driver No 67 0.132 17 0 0.0 10
DNAJC11 DNAJC11 Q9NVH1 DnaJ homolog subfamily C member 11 chr1 GO:0098798 Not Cancer Driver No 66 0.118 123 14 0.114 0
DNAJC15 DNAJC15 Q9Y5T4 DnaJ homolog subfamily C member 15 chr13 GO:0098798 Not Cancer Driver No 19 0.127 25 4 0.16 0
DNAJC19 DNAJC19 Q96DA6 Mitochondrial import inner membrane translocase subunit TIM14 chr3 GO:0098798 Not Cancer Driver No 19 0.164 27 6 0.222 0
GRPEL1 GRPEL1 Q9HAV7 GrpE protein homolog 1, mitochondrial chr4 GO:0098798 Not Cancer Driver No 22 0.101 88 7 0.08 0
GRPEL2 GRPEL2 Q8TAA5 GrpE protein homolog 2, mitochondrial chr5 GO:0098798 Not Cancer Driver No 17 0.076 45 3 0.067 0
HADHA HADHA P40939 Trifunctional enzyme subunit alpha, mitochondrial chr2 GO:0098798 Not Cancer Driver No 72 0.094 19 2 0.105 5
HADHB HADHB P55084 Trifunctional enzyme subunit beta, mitochondrial chr2 GO:0098798 Not Cancer Driver No 71 0.15 41 9 0.22 14
HSD17B10 HSD17B10 Q99714 3-hydroxyacyl-CoA dehydrogenase type-2 chrX GO:0098798 Not Cancer Driver No 27 0.103 15 3 0.2 11
HSPA9 HSPA9 P38646 Stress-70 protein, mitochondrial chr5 GO:0098798 Not Cancer Driver No 67 0.099 283 26 0.092 2
IDH3A IDH3A P50213 Isocitrate dehydrogenase [NAD] subunit alpha, mitochondrial chr15 GO:0098798 Not Cancer Driver No 41 0.112 47 11 0.234 0
IDH3B_ENST00000380843 IDH3B O43837 Isocitrate dehydrogenase [NAD] subunit beta, mitochondrial chr20 GO:0098798 Not Cancer Driver No 32 0.083 49 3 0.061 1
IDH3G IDH3G P51553 Isocitrate dehydrogenase [NAD] subunit gamma, mitochondrial chrX GO:0098798 Not Cancer Driver No 48 0.122 77 9 0.117 0
IMMP1L IMMP1L Q96LU5 Mitochondrial inner membrane protease subunit 1 chr11 GO:0098798 Not Cancer Driver No 20 0.12 3 0 0.0 0
IMMP2L_ENST00000452895 IMMP2L Q96T52 Mitochondrial inner membrane protease subunit 2 chr7 GO:0098798 Not Cancer Driver No 36 0.206 29 7 0.241 0
IMMT IMMT Q16891 MICOS complex subunit MIC60 chr2 GO:0098798 Not Cancer Driver No 97 0.128 400 50 0.125 0
KIAA0391 PRORP O15091 Mitochondrial ribonuclease P catalytic subunit chr14 GO:0098798 Not Cancer Driver No 62 0.106 60 12 0.2 0
MCCC1 MCCC1 Q96RQ3 Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial chr3 GO:0098798 Not Cancer Driver No 94 0.13 162 17 0.105 33
MCCC2 MCCC2 Q9HCC0 Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial chr5 GO:0098798 Not Cancer Driver No 60 0.107 25 2 0.08 52
MCU MCU Q8NE86 Calcium uniporter protein, mitochondrial chr10 GO:0098798 Not Cancer Driver No 41 0.117 13 0 0.0 0
MCUB MCUB Q9NWR8 Calcium uniporter regulatory subunit MCUb, mitochondrial chr4 GO:0098798 Not Cancer Driver No 33 0.098 24 1 0.042 0
MFN1 MFN1 Q8IWA4 Mitofusin-1 chr3 GO:0098798 Not Cancer Driver No 90 0.121 64 5 0.078 0
MICU1 MICU1 Q9BPX6 Calcium uptake protein 1, mitochondrial chr10 GO:0098798 Not Cancer Driver No 50 0.105 97 18 0.186 0
MICU2 MICU2 Q8IYU8 Calcium uptake protein 2, mitochondrial chr13 GO:0098798 Not Cancer Driver No 45 0.104 10 1 0.1 0
MICU3 MICU3 Q86XE3 Calcium uptake protein 3, mitochondrial chr8 GO:0098798 Not Cancer Driver No 72 0.136 89 8 0.09 0
MINOS1 MICOS10 Q5TGZ0 MICOS complex subunit MIC10 chr1 GO:0098798 Not Cancer Driver No 5 0.064 0 0 0.0 0
MRPS36 MRPS36 P82909 Alpha-ketoglutarate dehydrogenase component 4 chr5 GO:0098798 Not Cancer Driver No 12 0.117 103 12 0.117 0
MTX1 MTX1 Q13505 Metaxin-1 chr1 GO:0098798 Not Cancer Driver No 25 0.054 221 7 0.032 0
MTX2 MTX2 O75431 Metaxin-2 chr2 GO:0098798 Not Cancer Driver No 33 0.125 0 0 0.0 0
MTX3_ENST00000512528 MTX3 Q5HYI7 Metaxin-3 chr5 GO:0098798 Not Cancer Driver No 39 0.125 50 4 0.08 0
NDUFA4 NDUFA4 O00483 Cytochrome c oxidase subunit NDUFA4 chr7 GO:0098798 Not Cancer Driver No 14 0.173 4 0 0.0 0
NDUFA4L2 NDUFA4L2 Q9NRX3 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 4-like 2 chr12 GO:0098798 Not Cancer Driver No 9 0.103 8 0 0.0 0
PAM16_ENST00000576217 PAM16 Q9Y3D7 Mitochondrial import inner membrane translocase subunit TIM16 chr16 GO:0098798 Not Cancer Driver No 23 0.184 49 11 0.224 1
PDHA1_ENST00000422285 PDHA1 P08559 Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial chrX GO:0098798 Not Cancer Driver No 70 0.179 43 6 0.14 20
PDHB PDHB P11177 Pyruvate dehydrogenase E1 component subunit beta, mitochondrial chr3 GO:0098798 Not Cancer Driver No 32 0.089 4 0 0.0 2
PDHX PDHX O00330 Pyruvate dehydrogenase protein X component, mitochondrial chr11 GO:0098798 Not Cancer Driver No 62 0.124 179 28 0.156 0
PDK1_ENST00000282077 PDK1 Q15118 [Pyruvate dehydrogenase (acetyl-transferring)] kinase isozyme 1, mitochondrial chr2 GO:0098798 Not Cancer Driver No 52 0.119 50 10 0.2 0
PDK2 PDK2 Q15119 [Pyruvate dehydrogenase (acetyl-transferring)] kinase isozyme 2, mitochondrial chr17 GO:0098798 Not Cancer Driver No 45 0.111 35 4 0.114 0
PHB2 PHB2 Q99623 Prohibitin-2 chr12 GO:0098798 Not Cancer Driver No 31 0.104 26 4 0.154 0
PHB_ENST00000300408 PHB1 P35232 Prohibitin 1 chr17 GO:0098798 Not Cancer Driver No 37 0.136 4 1 0.25 0
PNPT1 PNPT1 Q8TCS8 Polyribonucleotide nucleotidyltransferase 1, mitochondrial chr2 GO:0098798 Not Cancer Driver No 86 0.11 115 10 0.087 2
POLG2 POLG2 Q9UHN1 DNA polymerase subunit gamma-2, mitochondrial chr17 GO:0098798 Not Cancer Driver No 64 0.132 46 4 0.087 3
POLG_ENST00000442287 POLG P54098 DNA polymerase subunit gamma-1 chr15 GO:0098798 Census Yes 139 0.112 421 42 0.1 73
POLRMT POLRMT O00411 DNA-directed RNA polymerase, mitochondrial chr19 GO:0098798 Not Cancer Driver No 188 0.153 253 31 0.123 0
PPIF PPIF P30405 Peptidyl-prolyl cis-trans isomerase F, mitochondrial chr10 GO:0098798 Not Cancer Driver No 19 0.092 43 4 0.093 0
SAMM50 SAMM50 Q9Y512 Sorting and assembly machinery component 50 homolog chr22 GO:0098798 Not Cancer Driver No 51 0.109 34 1 0.029 0
SDHA SDHA P31040 Succinate dehydrogenase [ubiquinone] flavoprotein subunit, mitochondrial chr5 GO:0098798 Census Yes 115 0.173 71 13 0.183 7
SDHB SDHB P21912 Succinate dehydrogenase [ubiquinone] iron-sulfur subunit, mitochondrial chr1 GO:0098798 Census Yes 37 0.132 17 3 0.176 23
SDHC SDHC Q99643 Succinate dehydrogenase cytochrome b560 subunit, mitochondrial chr1 GO:0098798 Census Yes 16 0.095 0 0 0.0 0
SDHD SDHD O14521 Succinate dehydrogenase [ubiquinone] cytochrome b small subunit, mitochondrial chr11 GO:0098798 Census Yes 22 0.138 0 0 0.0 10
SLC25A31 SLC25A31 Q9H0C2 ADP/ATP translocase 4 chr4 GO:0098798 Not Cancer Driver No 68 0.216 8 0 0.0 0
SLC25A4 SLC25A4 P12235 ADP/ATP translocase 1 chr4 GO:0098798 Not Cancer Driver No 24 0.081 0 0 0.0 9
SLC25A5 SLC25A5 P05141 ADP/ATP translocase 2 chrX GO:0098798 Not Cancer Driver No 41 0.138 0 0 0.0 0
SMDT1 SMDT1 Q9H4I9 Essential MCU regulator, mitochondrial chr22 GO:0098798 Not Cancer Driver No 6 0.056 6 0 0.0 0
SPG7 SPG7 Q9UQ90 Paraplegin chr16 GO:0098798 Not Cancer Driver No 97 0.122 181 29 0.16 4
SUCLG1 SUCLG1 P53597 Succinate--CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial chr2 GO:0098798 Not Cancer Driver No 48 0.139 57 8 0.14 3
SUCLG2_ENST00000307227 SUCLG2 Q96I99 Succinate--CoA ligase [GDP-forming] subunit beta, mitochondrial chr3 GO:0098798 Not Cancer Driver No 48 0.111 12 2 0.167 0
SUPV3L1 SUPV3L1 Q8IYB8 ATP-dependent RNA helicase SUPV3L1, mitochondrial chr10 GO:0098798 Not Cancer Driver No 72 0.092 140 12 0.086 0
TIMM10B TIMM10B Q9Y5J6 Mitochondrial import inner membrane translocase subunit Tim10 B chr11 GO:0098798 Not Cancer Driver No 6 0.058 24 3 0.125 0
TIMM10_ENST00000525587 TIMM10 P62072 Mitochondrial import inner membrane translocase subunit Tim10 chr11 GO:0098798 Not Cancer Driver No 6 0.067 43 6 0.14 0
TIMM13 TIMM13 Q9Y5L4 Mitochondrial import inner membrane translocase subunit Tim13 chr19 GO:0098798 Not Cancer Driver No 7 0.074 20 1 0.05 0
TIMM22 TIMM22 Q9Y584 Mitochondrial import inner membrane translocase subunit Tim22 chr17 GO:0098798 Not Cancer Driver No 20 0.103 56 7 0.125 1
TIMM29 TIMM29 Q9BSF4 Mitochondrial import inner membrane translocase subunit Tim29 chr19 GO:0098798 Not Cancer Driver No 9 0.035 4 0 0.0 0
TIMM8A_ENST00000647359 TIMM8A O60220 Mitochondrial import inner membrane translocase subunit Tim8 A chrX GO:0098798 Not Cancer Driver No 16 0.165 22 1 0.045 1
TIMM8B_ENST00000504148 TIMM8B Q9Y5J9 Mitochondrial import inner membrane translocase subunit Tim8 B chr11 GO:0098798 Not Cancer Driver No 9 0.108 8 1 0.125 0
TIMM9_ENST00000555593 TIMM9 Q9Y5J7 Mitochondrial import inner membrane translocase subunit Tim9 chr14 GO:0098798 Not Cancer Driver No 9 0.101 8 1 0.125 0
TOMM20 TOMM20 Q15388 Mitochondrial import receptor subunit TOM20 homolog chr1 GO:0098798 Not Cancer Driver No 8 0.055 25 1 0.04 0
TOMM20L TOMM20L Q6UXN7 TOMM20-like protein 1 chr14 GO:0098798 Not Cancer Driver No 10 0.066 38 3 0.079 0
TOMM22 TOMM22 Q9NS69 Mitochondrial import receptor subunit TOM22 homolog chr22 GO:0098798 Not Cancer Driver No 18 0.127 83 9 0.108 0
TOMM40L_ENST00000367987 TOMM40L Q969M1 Mitochondrial import receptor subunit TOM40B chr1 GO:0098798 Not Cancer Driver No 29 0.094 32 4 0.125 0
TOMM40_ENST00000405636 TOMM40 O96008 Mitochondrial import receptor subunit TOM40 homolog chr19 GO:0098798 Not Cancer Driver No 17 0.047 98 1 0.01 0
TOMM5_ENST00000321301 TOMM5 Q8N4H5 Mitochondrial import receptor subunit TOM5 homolog chr9 GO:0098798 Not Cancer Driver No 4 0.078 0 0 0.0 0
TOMM7 TOMM7 Q9P0U1 Mitochondrial import receptor subunit TOM7 homolog chr7 GO:0098798 Not Cancer Driver No 7 0.127 0 0 0.0 0
TOMM70 TOMM70 O94826 Mitochondrial import receptor subunit TOM70 chr3 GO:0098798 Not Cancer Driver No 59 0.097 140 8 0.057 0
TRMT10B TRMT10B Q6PF06 tRNA methyltransferase 10 homolog B chr9 GO:0098798 Not Cancer Driver No 35 0.111 75 13 0.173 0
TRMT10C TRMT10C Q7L0Y3 tRNA methyltransferase 10 homolog C chr3 GO:0098798 Not Cancer Driver No 56 0.139 59 10 0.169 2
UQCRC2 UQCRC2 P22695 Cytochrome b-c1 complex subunit 2, mitochondrial chr16 GO:0098798 Not Cancer Driver No 53 0.117 48 13 0.271 1
UQCRFS1 UQCRFS1 P47985 Cytochrome b-c1 complex subunit Rieske, mitochondrial chr19 GO:0098798 Not Cancer Driver No 43 0.157 47 4 0.085 1
VDAC1_ENST00000395047 VDAC1 P21796 Voltage-dependent anion-selective channel protein 1 chr5 GO:0098798 Not Cancer Driver No 38 0.134 36 4 0.111 0