Total number of protein in "GO:0005759" GO term: 374
| Identifier | UniProt Gene | UniProt Accession | UniProt Name | Chromosome | GO term | Database | Cancer Driver | Number of missense mutations | Missense mutation per residues | Number of disordered residues | Number of mutations in disordered regions | Disordered missense mutations per residues | Number of OMIM mutation |
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| AADAT_ENST00000515480 | AADAT | Q8N5Z0 | Kynurenine/alpha-aminoadipate aminotransferase, mitochondrial | chr4 | GO:0005759 | Not Cancer Driver | No | 48 | 0.113 | 71 | 10 | 0.141 | 0 |
| AASS | AASS | Q9UDR5 | Alpha-aminoadipic semialdehyde synthase, mitochondrial | chr7 | GO:0005759 | Not Cancer Driver | No | 161 | 0.174 | 18 | 3 | 0.167 | 0 |
| ABAT_ENST00000268251 | ABAT | P80404 | 4-aminobutyrate aminotransferase, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 84 | 0.168 | 28 | 5 | 0.179 | 1 |
| ABCE1 | ABCE1 | P61221 | ATP-binding cassette sub-family E member 1 | chr4 | GO:0005759 | Not Cancer Driver | No | 74 | 0.124 | 36 | 6 | 0.167 | 0 |
| ABHD10 | ABHD10 | Q9NUJ1 | Palmitoyl-protein thioesterase ABHD10, mitochondrial | chr3 | GO:0005759 | Not Cancer Driver | No | 38 | 0.124 | 7 | 2 | 0.286 | 0 |
| ACAA2 | ACAA2 | P42765 | 3-ketoacyl-CoA thiolase, mitochondrial | chr18 | GO:0005759 | Not Cancer Driver | No | 42 | 0.106 | 51 | 2 | 0.039 | 0 |
| ACAD10_ENST00000313698 | ACAD10 | Q6JQN1 | Acyl-CoA dehydrogenase family member 10 | chr12 | GO:0005759 | Not Cancer Driver | No | 143 | 0.135 | 91 | 19 | 0.209 | 0 |
| ACAD8 | ACAD8 | Q9UKU7 | Isobutyryl-CoA dehydrogenase, mitochondrial | chr11 | GO:0005759 | Not Cancer Driver | No | 55 | 0.133 | 13 | 1 | 0.077 | 9 |
| ACADL | ACADL | P28330 | Long-chain specific acyl-CoA dehydrogenase, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 63 | 0.147 | 51 | 3 | 0.059 | 0 |
| ACADM_ENST00000370841 | ACADM | P11310 | Medium-chain specific acyl-CoA dehydrogenase, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 61 | 0.145 | 41 | 5 | 0.122 | 19 |
| ACADS | ACADS | P16219 | Short-chain specific acyl-CoA dehydrogenase, mitochondrial | chr12 | GO:0005759 | Not Cancer Driver | No | 53 | 0.129 | 16 | 3 | 0.188 | 10 |
| ACADSB | ACADSB | P45954 | Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial | chr10 | GO:0005759 | Not Cancer Driver | No | 59 | 0.137 | 16 | 3 | 0.188 | 1 |
| ACADVL_ENST00000356839 | ACADVL | P49748 | Very long-chain specific acyl-CoA dehydrogenase, mitochondrial | chr17 | GO:0005759 | Not Cancer Driver | No | 50 | 0.076 | 100 | 5 | 0.05 | 37 |
| ACAT1 | ACAT1 | P24752 | Acetyl-CoA acetyltransferase, mitochondrial | chr11 | GO:0005759 | Not Cancer Driver | No | 45 | 0.105 | 32 | 1 | 0.031 | 10 |
| ACO2 | ACO2 | Q99798 | Aconitate hydratase, mitochondrial | chr22 | GO:0005759 | Not Cancer Driver | No | 94 | 0.121 | 172 | 19 | 0.11 | 5 |
| ACOT11 | ACOT11 | Q8WXI4 | Acyl-coenzyme A thioesterase 11 | chr1 | GO:0005759 | Not Cancer Driver | No | 88 | 0.145 | 110 | 19 | 0.173 | 0 |
| ACOT13 | ACOT13 | Q9NPJ3 | Acyl-coenzyme A thioesterase 13 | chr6 | GO:0005759 | Not Cancer Driver | No | 15 | 0.107 | 23 | 2 | 0.087 | 0 |
| ACOT2 | ACOT2 | P49753 | Acyl-coenzyme A thioesterase 2, mitochondrial | chr14 | GO:0005759 | Not Cancer Driver | No | 49 | 0.101 | 35 | 5 | 0.143 | 0 |
| ACOT9_ENST00000336430 | ACOT9 | Q9Y305 | Acyl-coenzyme A thioesterase 9, mitochondrial | chrX | GO:0005759 | Not Cancer Driver | No | 45 | 0.103 | 45 | 3 | 0.067 | 0 |
| ACP6 | ACP6 | Q9NPH0 | Lysophosphatidic acid phosphatase type 6 | chr1 | GO:0005759 | Not Cancer Driver | No | 53 | 0.124 | 40 | 5 | 0.125 | 0 |
| ACSF2_ENST00000300441 | ACSF2 | Q96CM8 | Medium-chain acyl-CoA ligase ACSF2, mitochondrial | chr17 | GO:0005759 | Not Cancer Driver | No | 73 | 0.119 | 55 | 10 | 0.182 | 0 |
| ACSF3_ENST00000406948 | ACSF3 | Q4G176 | Malonate--CoA ligase ACSF3, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 87 | 0.151 | 48 | 11 | 0.229 | 9 |
| ACSM1_ENST00000520010 | ACSM1 | Q08AH1 | Acyl-coenzyme A synthetase ACSM1, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 134 | 0.232 | 64 | 16 | 0.25 | 0 |
| ACSM2A_ENST00000219054 | ACSM2A | Q08AH3 | Acyl-coenzyme A synthetase ACSM2A, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 200 | 0.347 | 48 | 24 | 0.5 | 0 |
| ACSM2B | ACSM2B | Q68CK6 | Acyl-coenzyme A synthetase ACSM2B, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 230 | 0.399 | 45 | 23 | 0.511 | 0 |
| ACSM3 | ACSM3 | Q53FZ2 | Acyl-coenzyme A synthetase ACSM3, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 95 | 0.162 | 79 | 8 | 0.101 | 0 |
| ACSM4 | ACSM4 | P0C7M7 | Acyl-coenzyme A synthetase ACSM4, mitochondrial | chr12 | GO:0005759 | Not Cancer Driver | No | 128 | 0.221 | 20 | 9 | 0.45 | 0 |
| ACSM5 | ACSM5 | Q6NUN0 | Acyl-coenzyme A synthetase ACSM5, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 152 | 0.263 | 84 | 27 | 0.321 | 0 |
| ACSM6_ENST00000394005 | ACSM6 | Q6P461 | Acyl-coenzyme A synthetase ACSM6, mitochondrial | chr10 | GO:0005759 | Not Cancer Driver | No | 56 | 0.117 | 0 | 0 | 0.0 | 0 |
| ACSS1 | ACSS1 | Q9NUB1 | Acetyl-coenzyme A synthetase 2-like, mitochondrial | chr20 | GO:0005759 | Not Cancer Driver | No | 79 | 0.115 | 76 | 6 | 0.079 | 0 |
| ACSS2_ENST00000360596 | ACSS2 | Q9NR19 | Acetyl-coenzyme A synthetase, cytoplasmic | chr20 | GO:0005759 | Not Cancer Driver | No | 62 | 0.088 | 111 | 6 | 0.054 | 0 |
| ACSS3 | ACSS3 | Q9H6R3 | Acyl-CoA synthetase short-chain family member 3, mitochondrial | chr12 | GO:0005759 | Not Cancer Driver | No | 194 | 0.283 | 63 | 10 | 0.159 | 0 |
| ADHFE1 | ADHFE1 | Q8IWW8 | Hydroxyacid-oxoacid transhydrogenase, mitochondrial | chr8 | GO:0005759 | Not Cancer Driver | No | 63 | 0.135 | 37 | 8 | 0.216 | 0 |
| ADPRHL2 | ADPRS | Q9NX46 | ADP-ribosylhydrolase ARH3 | chr1 | GO:0005759 | Not Cancer Driver | No | 32 | 0.088 | 49 | 4 | 0.082 | 1 |
| AGXT2 | AGXT2 | Q9BYV1 | Alanine--glyoxylate aminotransferase 2, mitochondrial | chr5 | GO:0005759 | Not Cancer Driver | No | 136 | 0.265 | 11 | 5 | 0.455 | 0 |
| AK3 | AK3 | Q9UIJ7 | GTP:AMP phosphotransferase AK3, mitochondrial | chr9 | GO:0005759 | Not Cancer Driver | No | 23 | 0.101 | 33 | 3 | 0.091 | 0 |
| AK4 | AK4 | P27144 | Adenylate kinase 4, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 26 | 0.117 | 24 | 3 | 0.125 | 0 |
| ALAS1_ENST00000484952 | ALAS1 | P13196 | 5-aminolevulinate synthase, non-specific, mitochondrial | chr3 | GO:0005759 | Not Cancer Driver | No | 68 | 0.106 | 177 | 16 | 0.09 | 0 |
| ALAS2 | ALAS2 | P22557 | 5-aminolevulinate synthase, erythroid-specific, mitochondrial | chrX | GO:0005759 | Not Cancer Driver | No | 107 | 0.182 | 87 | 17 | 0.195 | 24 |
| ALDH1B1 | ALDH1B1 | P30837 | Aldehyde dehydrogenase X, mitochondrial | chr9 | GO:0005759 | Not Cancer Driver | No | 94 | 0.182 | 54 | 11 | 0.204 | 0 |
| ALDH1L2 | ALDH1L2 | Q3SY69 | Mitochondrial 10-formyltetrahydrofolate dehydrogenase | chr12 | GO:0005759 | Not Cancer Driver | No | 108 | 0.117 | 81 | 12 | 0.148 | 0 |
| ALDH2 | ALDH2 | P05091 | Aldehyde dehydrogenase, mitochondrial | chr12 | GO:0005759 | Census | Yes | 60 | 0.116 | 44 | 1 | 0.023 | 0 |
| ALDH4A1 | ALDH4A1 | P30038 | Delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 63 | 0.112 | 46 | 9 | 0.196 | 1 |
| ALDH5A1_ENST00000357578 | ALDH5A1 | P51649 | Succinate-semialdehyde dehydrogenase, mitochondrial | chr6 | GO:0005759 | Not Cancer Driver | No | 64 | 0.12 | 31 | 7 | 0.226 | 12 |
| ALDH6A1 | ALDH6A1 | Q02252 | Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial | chr14 | GO:0005759 | Not Cancer Driver | No | 54 | 0.101 | 83 | 11 | 0.133 | 1 |
| ALDH7A1 | ALDH7A1 | P49419 | Alpha-aminoadipic semialdehyde dehydrogenase | chr5 | GO:0005759 | Not Cancer Driver | No | 52 | 0.096 | 26 | 1 | 0.038 | 8 |
| ALKBH7 | ALKBH7 | Q9BT30 | Alpha-ketoglutarate-dependent dioxygenase alkB homolog 7, mitochondrial | chr19 | GO:0005759 | Not Cancer Driver | No | 21 | 0.095 | 28 | 1 | 0.036 | 0 |
| AMT | AMT | P48728 | Aminomethyltransferase, mitochondrial | chr3 | GO:0005759 | Not Cancer Driver | No | 37 | 0.092 | 33 | 6 | 0.182 | 11 |
| ARG2 | ARG2 | P78540 | Arginase-2, mitochondrial | chr14 | GO:0005759 | Not Cancer Driver | No | 25 | 0.071 | 58 | 3 | 0.052 | 0 |
| ARHGAP11B | ARHGAP11B | Q3KRB8 | Inactive Rho GTPase-activating protein 11B | chr15 | GO:0005759 | Not Cancer Driver | No | 20 | 0.075 | 17 | 1 | 0.059 | 0 |
| ARL2 | ARL2 | P36404 | ADP-ribosylation factor-like protein 2 | chr11 | GO:0005759 | Not Cancer Driver | No | 19 | 0.103 | 0 | 0 | 0.0 | 1 |
| ARL2BP | ARL2BP | Q9Y2Y0 | ADP-ribosylation factor-like protein 2-binding protein | chr16 | GO:0005759 | Not Cancer Driver | No | 16 | 0.098 | 5 | 0 | 0.0 | 1 |
| ATG4D | ATG4D | Q86TL0 | Cysteine protease ATG4D | chr19 | GO:0005759 | Not Cancer Driver | No | 70 | 0.148 | 106 | 12 | 0.113 | 0 |
| ATP5F1A_ENST00000282050 | ATP5F1A | P25705 | ATP synthase subunit alpha, mitochondrial | chr18 | GO:0005759 | Not Cancer Driver | No | 66 | 0.119 | 23 | 5 | 0.217 | 2 |
| ATP5F1B | ATP5F1B | P06576 | ATP synthase subunit beta, mitochondrial | chr12 | GO:0005759 | Not Cancer Driver | No | 60 | 0.113 | 85 | 8 | 0.094 | 0 |
| ATP5F1C | ATP5F1C | P36542 | ATP synthase subunit gamma, mitochondrial | chr10 | GO:0005759 | Not Cancer Driver | No | 39 | 0.131 | 11 | 0 | 0.0 | 0 |
| ATP5F1D_ENST00000591660 | ATP5F1D | P30049 | ATP synthase subunit delta, mitochondrial | chr19 | GO:0005759 | Not Cancer Driver | No | 7 | 0.042 | 5 | 1 | 0.2 | 2 |
| ATP5F1E_ENST00000395663 | ATP5F1E | P56381 | ATP synthase subunit epsilon, mitochondrial | chr20 | GO:0005759 | Not Cancer Driver | No | 3 | 0.059 | 1 | 0 | 0.0 | 1 |
| ATP5PB | ATP5PB | P24539 | ATP synthase F(0) complex subunit B1, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 37 | 0.145 | 2 | 0 | 0.0 | 0 |
| ATXN3 | ATXN3 | P54252 | Ataxin-3 | chr14 | GO:0005759 | Not Cancer Driver | No | 46 | 0.127 | 181 | 24 | 0.133 | 0 |
| AUH | AUH | Q13825 | Methylglutaconyl-CoA hydratase, mitochondrial | chr9 | GO:0005759 | Not Cancer Driver | No | 34 | 0.1 | 29 | 0 | 0.0 | 1 |
| BCAT2 | BCAT2 | O15382 | Branched-chain-amino-acid aminotransferase, mitochondrial | chr19 | GO:0005759 | Not Cancer Driver | No | 54 | 0.138 | 19 | 0 | 0.0 | 2 |
| BCKDHA | BCKDHA | P12694 | 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial | chr19 | GO:0005759 | Not Cancer Driver | No | 53 | 0.119 | 121 | 18 | 0.149 | 11 |
| BCKDHB | BCKDHB | P21953 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial | chr6 | GO:0005759 | Not Cancer Driver | No | 47 | 0.12 | 23 | 3 | 0.13 | 5 |
| BCKDK | BCKDK | O14874 | [3-methyl-2-oxobutanoate dehydrogenase [lipoamide]] kinase, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 62 | 0.15 | 39 | 3 | 0.077 | 3 |
| BCL2L1 | BCL2L1 | Q07817 | Bcl-2-like protein 1 | chr20 | GO:0005759 | Not Cancer Driver | No | 29 | 0.124 | 55 | 3 | 0.055 | 0 |
| BCO2 | BCO2 | Q9BYV7 | Carotenoid-cleaving dioxygenase, mitochondrial | chr11 | GO:0005759 | Not Cancer Driver | No | 79 | 0.136 | 14 | 1 | 0.071 | 0 |
| BDH1 | BDH1 | Q02338 | D-beta-hydroxybutyrate dehydrogenase, mitochondrial | chr3 | GO:0005759 | Not Cancer Driver | No | 44 | 0.128 | 15 | 1 | 0.067 | 0 |
| BLOC1S1 | BLOC1S1 | P78537 | Biogenesis of lysosome-related organelles complex 1 subunit 1 | chr12 | GO:0005759 | Not Cancer Driver | No | 12 | 0.078 | 76 | 2 | 0.026 | 0 |
| BTD_ENST00000643237 | BTD | P43251 | Biotinidase | chr3 | GO:0005759 | Not Cancer Driver | No | 63 | 0.116 | 13 | 1 | 0.077 | 9 |
| C12orf10 | MYG1 | Q9HB07 | MYG1 exonuclease | chr12 | GO:0005759 | Not Cancer Driver | No | 30 | 0.08 | 95 | 9 | 0.095 | 0 |
| C1QBP | C1QBP | Q07021 | Complement component 1 Q subcomponent-binding protein, mitochondrial | chr17 | GO:0005759 | Not Cancer Driver | No | 14 | 0.05 | 103 | 6 | 0.058 | 2 |
| C2orf69 | C2orf69 | Q8N8R5 | Mitochondrial protein C2orf69 | chr2 | GO:0005759 | Not Cancer Driver | No | 32 | 0.083 | 80 | 1 | 0.013 | 0 |
| C6orf203_ENST00000405204 | MTRES1 | Q9P0P8 | Mitochondrial transcription rescue factor 1 | chr6 | GO:0005759 | Not Cancer Driver | No | 28 | 0.117 | 45 | 4 | 0.089 | 0 |
| CA5A | CA5A | P35218 | Carbonic anhydrase 5A, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 43 | 0.141 | 20 | 3 | 0.15 | 1 |
| CA5B_ENST00000454127 | CA5B | Q9Y2D0 | Carbonic anhydrase 5B, mitochondrial | chrX | GO:0005759 | Not Cancer Driver | No | 40 | 0.126 | 28 | 2 | 0.071 | 0 |
| CARS2 | CARS2 | Q9HA77 | Probable cysteine--tRNA ligase, mitochondrial | chr13 | GO:0005759 | Not Cancer Driver | No | 51 | 0.09 | 87 | 8 | 0.092 | 1 |
| CASQ1 | CASQ1 | P31415 | Calsequestrin-1 | chr1 | GO:0005759 | Not Cancer Driver | No | 77 | 0.194 | 110 | 18 | 0.164 | 4 |
| CBR4 | CBR4 | Q8N4T8 | 3-oxoacyl-[acyl-carrier-protein] reductase | chr4 | GO:0005759 | Not Cancer Driver | No | 15 | 0.063 | 4 | 0 | 0.0 | 0 |
| CCAR2 | CCAR2 | Q8N163 | Cell cycle and apoptosis regulator protein 2 | chr8 | GO:0005759 | Not Cancer Driver | No | 102 | 0.111 | 528 | 62 | 0.117 | 0 |
| CCNB1 | CCNB1 | P14635 | G2/mitotic-specific cyclin-B1 | chr5 | GO:0005759 | Not Cancer Driver | No | 49 | 0.113 | 145 | 14 | 0.097 | 0 |
| CDK1 | CDK1 | P06493 | Cyclin-dependent kinase 1 | chr10 | GO:0005759 | Not Cancer Driver | No | 40 | 0.135 | 1 | 0 | 0.0 | 0 |
| CHPF | CHPF | Q8IZ52 | Chondroitin sulfate synthase 2 | chr2 | GO:0005759 | Not Cancer Driver | No | 88 | 0.114 | 194 | 18 | 0.093 | 0 |
| CLPP | CLPP | Q16740 | ATP-dependent Clp protease proteolytic subunit, mitochondrial | chr19 | GO:0005759 | Not Cancer Driver | No | 22 | 0.079 | 83 | 9 | 0.108 | 3 |
| CLPX | CLPX | O76031 | ATP-dependent Clp protease ATP-binding subunit clpX-like, mitochondrial | chr15 | GO:0005759 | Not Cancer Driver | No | 66 | 0.104 | 195 | 22 | 0.113 | 1 |
| COASY_ENST00000421097 | COASY | Q13057 | Bifunctional coenzyme A synthase | chr17 | GO:0005759 | Not Cancer Driver | No | 57 | 0.101 | 50 | 4 | 0.08 | 1 |
| COQ3 | COQ3 | Q9NZJ6 | Ubiquinone biosynthesis O-methyltransferase, mitochondrial | chr6 | GO:0005759 | Not Cancer Driver | No | 47 | 0.127 | 22 | 5 | 0.227 | 0 |
| COQ5 | COQ5 | Q5HYK3 | 2-methoxy-6-polyprenyl-1,4-benzoquinol methylase, mitochondrial | chr12 | GO:0005759 | Not Cancer Driver | No | 45 | 0.138 | 15 | 2 | 0.133 | 0 |
| CPS1_ENST00000233072 | CPS1 | P31327 | Carbamoyl-phosphate synthase [ammonia], mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 368 | 0.245 | 73 | 22 | 0.301 | 140 |
| CS | CS | O75390 | Citrate synthase, mitochondrial | chr12 | GO:0005759 | Not Cancer Driver | No | 50 | 0.107 | 13 | 2 | 0.154 | 0 |
| CYP11A1 | CYP11A1 | P05108 | Cholesterol side-chain cleavage enzyme, mitochondrial | chr15 | GO:0005759 | Not Cancer Driver | No | 92 | 0.177 | 27 | 6 | 0.222 | 6 |
| CYP27A1 | CYP27A1 | Q02318 | Sterol 26-hydroxylase, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 69 | 0.13 | 47 | 11 | 0.234 | 7 |
| D2HGDH | D2HGDH | Q8N465 | D-2-hydroxyglutarate dehydrogenase, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 61 | 0.117 | 46 | 1 | 0.022 | 0 |
| DARS2 | DARS2 | Q6PI48 | Aspartate--tRNA ligase, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 63 | 0.098 | 91 | 11 | 0.121 | 11 |
| DBT | DBT | P11182 | Lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 64 | 0.133 | 81 | 11 | 0.136 | 3 |
| DECR1 | DECR1 | Q16698 | 2,4-dienoyl-CoA reductase [(3E)-enoyl-CoA-producing], mitochondrial | chr8 | GO:0005759 | Not Cancer Driver | No | 38 | 0.113 | 11 | 0 | 0.0 | 0 |
| DGLUCY_ENST00000428926 | DGLUCY | Q7Z3D6 | D-glutamate cyclase, mitochondrial | chr14 | GO:0005759 | Not Cancer Driver | No | 78 | 0.127 | 120 | 14 | 0.117 | 0 |
| DGUOK | DGUOK | Q16854 | Deoxyguanosine kinase, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 25 | 0.09 | 17 | 1 | 0.059 | 6 |
| DHFR2_ENST00000314636 | DHFR2 | Q86XF0 | Dihydrofolate reductase 2, mitochondrial | chr3 | GO:0005759 | Not Cancer Driver | No | 25 | 0.134 | 20 | 0 | 0.0 | 0 |
| DHRS2_ENST00000250383 | DHRS2 | Q13268 | Dehydrogenase/reductase SDR family member 2, mitochondrial | chr14 | GO:0005759 | Not Cancer Driver | No | 47 | 0.168 | 0 | 0 | 0.0 | 0 |
| DHTKD1 | DHTKD1 | Q96HY7 | 2-oxoadipate dehydrogenase complex component E1 | chr10 | GO:0005759 | Not Cancer Driver | No | 119 | 0.129 | 117 | 15 | 0.128 | 2 |
| DIMT1 | DIMT1 | Q9UNQ2 | Probable dimethyladenosine transferase | chr5 | GO:0005759 | Not Cancer Driver | No | 28 | 0.089 | 37 | 2 | 0.054 | 0 |
| DLAT | DLAT | P10515 | Dihydrolipoyllysine-residue acetyltransferase component of pyruvate dehydrogenase complex, mitochondrial | chr11 | GO:0005759 | Not Cancer Driver | No | 63 | 0.097 | 294 | 42 | 0.143 | 0 |
| DLD | DLD | P09622 | Dihydrolipoyl dehydrogenase, mitochondrial | chr7 | GO:0005759 | Not Cancer Driver | No | 67 | 0.132 | 17 | 0 | 0.0 | 10 |
| DLST | DLST | P36957 | Dihydrolipoyllysine-residue succinyltransferase component of 2-oxoglutarate dehydrogenase complex, mitochondrial | chr14 | GO:0005759 | Not Cancer Driver | No | 53 | 0.117 | 190 | 32 | 0.168 | 1 |
| DMGDH | DMGDH | Q9UI17 | Dimethylglycine dehydrogenase, mitochondrial | chr5 | GO:0005759 | Not Cancer Driver | No | 155 | 0.179 | 74 | 12 | 0.162 | 1 |
| DNAJA3 | DNAJA3 | Q96EY1 | DnaJ homolog subfamily A member 3, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 50 | 0.104 | 152 | 21 | 0.138 | 0 |
| DUSP21 | DUSP21 | Q9H596 | Dual specificity protein phosphatase 21 | chrX | GO:0005759 | Not Cancer Driver | No | 49 | 0.258 | 0 | 0 | 0.0 | 0 |
| EARS2_ENST00000449606 | EARS2 | Q5JPH6 | Probable glutamate--tRNA ligase, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 56 | 0.107 | 99 | 14 | 0.141 | 14 |
| ECHS1 | ECHS1 | P30084 | Enoyl-CoA hydratase, mitochondrial | chr10 | GO:0005759 | Not Cancer Driver | No | 51 | 0.176 | 7 | 1 | 0.143 | 14 |
| ECI1 | ECI1 | P42126 | Enoyl-CoA delta isomerase 1, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 27 | 0.089 | 14 | 0 | 0.0 | 0 |
| ELAC2 | ELAC2 | Q9BQ52 | Zinc phosphodiesterase ELAC protein 2 | chr17 | GO:0005759 | Not Cancer Driver | No | 86 | 0.104 | 208 | 30 | 0.144 | 10 |
| ERAL1 | ERAL1 | O75616 | GTPase Era, mitochondrial | chr17 | GO:0005759 | Not Cancer Driver | No | 32 | 0.073 | 81 | 6 | 0.074 | 1 |
| ERBB4 | ERBB4 | Q15303 | Receptor tyrosine-protein kinase erbB-4 | chr2 | GO:0005759 | Census, Compendium | Yes | 428 | 0.327 | 323 | 116 | 0.359 | 2 |
| ETFA | ETFA | P13804 | Electron transfer flavoprotein subunit alpha, mitochondrial | chr15 | GO:0005759 | Not Cancer Driver | No | 30 | 0.09 | 34 | 2 | 0.059 | 3 |
| ETFBKMT_ENST00000412352 | ETFBKMT | Q8IXQ9 | Electron transfer flavoprotein beta subunit lysine methyltransferase | chr12 | GO:0005759 | Not Cancer Driver | No | 25 | 0.095 | 0 | 0 | 0.0 | 0 |
| ETFB_ENST00000309244 | ETFB | P38117 | Electron transfer flavoprotein subunit beta | chr19 | GO:0005759 | Not Cancer Driver | No | 37 | 0.145 | 38 | 4 | 0.105 | 2 |
| ETFDH | ETFDH | Q16134 | Electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial | chr4 | GO:0005759 | Not Cancer Driver | No | 61 | 0.099 | 64 | 4 | 0.062 | 12 |
| ETHE1 | ETHE1 | O95571 | Persulfide dioxygenase ETHE1, mitochondrial | chr19 | GO:0005759 | Not Cancer Driver | No | 21 | 0.083 | 6 | 0 | 0.0 | 9 |
| ETNPPL | ETNPPL | Q8TBG4 | Ethanolamine-phosphate phospho-lyase | chr4 | GO:0005759 | Not Cancer Driver | No | 92 | 0.184 | 80 | 14 | 0.175 | 0 |
| EXD2 | EXD2 | Q9NVH0 | Exonuclease 3'-5' domain-containing protein 2 | chr14 | GO:0005759 | Not Cancer Driver | No | 58 | 0.093 | 176 | 15 | 0.085 | 0 |
| FAHD1_ENST00000427358 | FAHD1 | Q6P587 | Acylpyruvase FAHD1, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 15 | 0.067 | 12 | 0 | 0.0 | 0 |
| FARS2_ENST00000274680 | FARS2 | O95363 | Phenylalanine--tRNA ligase, mitochondrial | chr6 | GO:0005759 | Not Cancer Driver | No | 66 | 0.146 | 73 | 17 | 0.233 | 4 |
| FASTK | FASTK | Q14296 | Fas-activated serine/threonine kinase | chr7 | GO:0005759 | Not Cancer Driver | No | 65 | 0.118 | 143 | 12 | 0.084 | 0 |
| FASTKD1 | FASTKD1 | Q53R41 | FAST kinase domain-containing protein 1, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 125 | 0.148 | 0 | 0 | 0.0 | 0 |
| FASTKD2_ENST00000402774 | FASTKD2 | Q9NYY8 | FAST kinase domain-containing protein 2, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 74 | 0.104 | 30 | 2 | 0.067 | 0 |
| FASTKD3 | FASTKD3 | Q14CZ7 | FAST kinase domain-containing protein 3, mitochondrial | chr5 | GO:0005759 | Not Cancer Driver | No | 106 | 0.16 | 6 | 1 | 0.167 | 0 |
| FASTKD5 | FASTKD5 | Q7L8L6 | FAST kinase domain-containing protein 5, mitochondrial | chr20 | GO:0005759 | Not Cancer Driver | No | 86 | 0.113 | 94 | 8 | 0.085 | 0 |
| FDX1 | FDX1 | P10109 | Adrenodoxin, mitochondrial | chr11 | GO:0005759 | Not Cancer Driver | No | 12 | 0.065 | 61 | 2 | 0.033 | 0 |
| FDX2 | FDX2 | Q6P4F2 | Ferredoxin-2, mitochondrial | chr19 | GO:0005759 | Not Cancer Driver | No | 26 | 0.14 | 102 | 14 | 0.137 | 1 |
| FDXR_ENST00000293195 | FDXR | P22570 | NADPH:adrenodoxin oxidoreductase, mitochondrial | chr17 | GO:0005759 | Not Cancer Driver | No | 68 | 0.138 | 102 | 14 | 0.137 | 4 |
| FECH_ENST00000262093 | FECH | P22830 | Ferrochelatase, mitochondrial | chr18 | GO:0005759 | Not Cancer Driver | No | 52 | 0.123 | 57 | 8 | 0.14 | 23 |
| FH | FH | P07954 | Fumarate hydratase, mitochondrial | chr1 | GO:0005759 | Census, Compendium | Yes | 67 | 0.131 | 76 | 5 | 0.066 | 13 |
| FLAD1 | FLAD1 | Q8NFF5 | FAD synthase | chr1 | GO:0005759 | Not Cancer Driver | No | 81 | 0.138 | 59 | 6 | 0.102 | 1 |
| FOXO3 | FOXO3 | O43524 | Forkhead box protein O3 | chr6 | GO:0005759 | Census, Compendium | Yes | 70 | 0.104 | 595 | 68 | 0.114 | 0 |
| FPGS | FPGS | Q05932 | Folylpolyglutamate synthase, mitochondrial | chr9 | GO:0005759 | Not Cancer Driver | No | 68 | 0.116 | 141 | 18 | 0.128 | 0 |
| FTMT | FTMT | Q8N4E7 | Ferritin, mitochondrial | chr5 | GO:0005759 | Not Cancer Driver | No | 96 | 0.397 | 93 | 33 | 0.355 | 0 |
| FXN | FXN | Q16595 | Frataxin, mitochondrial | chr9 | GO:0005759 | Not Cancer Driver | No | 16 | 0.076 | 73 | 0 | 0.0 | 8 |
| GADD45GIP1 | GADD45GIP1 | Q8TAE8 | Growth arrest and DNA damage-inducible proteins-interacting protein 1 | chr19 | GO:0005759 | Not Cancer Driver | No | 19 | 0.086 | 193 | 19 | 0.098 | 0 |
| GARS | GARS1 | P41250 | Glycine--tRNA ligase | chr7 | GO:0005759 | Not Cancer Driver | No | 61 | 0.083 | 75 | 9 | 0.12 | 17 |
| GCDH_ENST00000591470 | GCDH | Q92947 | Glutaryl-CoA dehydrogenase, mitochondrial | chr19 | GO:0005759 | Not Cancer Driver | No | 57 | 0.13 | 37 | 5 | 0.135 | 58 |
| GCSH | GCSH | P23434 | Glycine cleavage system H protein, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 15 | 0.087 | 25 | 0 | 0.0 | 0 |
| GFM1_ENST00000486715 | GFM1 | Q96RP9 | Elongation factor G, mitochondrial | chr3 | GO:0005759 | Not Cancer Driver | No | 74 | 0.099 | 79 | 7 | 0.089 | 4 |
| GFM2_ENST00000509430 | GFM2 | Q969S9 | Ribosome-releasing factor 2, mitochondrial | chr5 | GO:0005759 | Not Cancer Driver | No | 75 | 0.096 | 100 | 10 | 0.1 | 2 |
| GLDC | GLDC | P23378 | Glycine dehydrogenase (decarboxylating), mitochondrial | chr9 | GO:0005759 | Not Cancer Driver | No | 152 | 0.149 | 112 | 7 | 0.062 | 22 |
| GLRX2_ENST00000367439 | GLRX2 | Q9NS18 | Glutaredoxin-2, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 12 | 0.073 | 10 | 1 | 0.1 | 0 |
| GLRX5 | GLRX5 | Q86SX6 | Glutaredoxin-related protein 5, mitochondrial | chr14 | GO:0005759 | Not Cancer Driver | No | 7 | 0.045 | 23 | 0 | 0.0 | 2 |
| GLS | GLS | O94925 | Glutaminase kidney isoform, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 71 | 0.106 | 187 | 9 | 0.048 | 3 |
| GLS2 | GLS2 | Q9UI32 | Glutaminase liver isoform, mitochondrial | chr12 | GO:0005759 | Not Cancer Driver | No | 57 | 0.095 | 108 | 9 | 0.083 | 0 |
| GLUD1 | GLUD1 | P00367 | Glutamate dehydrogenase 1, mitochondrial | chr10 | GO:0005759 | Not Cancer Driver | No | 50 | 0.09 | 107 | 14 | 0.131 | 13 |
| GLUD2 | GLUD2 | P49448 | Glutamate dehydrogenase 2, mitochondrial | chrX | GO:0005759 | Not Cancer Driver | No | 145 | 0.26 | 117 | 37 | 0.316 | 0 |
| GLYAT | GLYAT | Q6IB77 | Glycine N-acyltransferase | chr11 | GO:0005759 | Not Cancer Driver | No | 75 | 0.253 | 9 | 2 | 0.222 | 0 |
| GOT2 | GOT2 | P00505 | Aspartate aminotransferase, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 61 | 0.142 | 25 | 3 | 0.12 | 1 |
| GPT2 | GPT2 | Q8TD30 | Alanine aminotransferase 2 | chr16 | GO:0005759 | Not Cancer Driver | No | 61 | 0.117 | 68 | 5 | 0.074 | 1 |
| GPX1_ENST00000620890 | GPX1 | P07203 | Glutathione peroxidase 1 | chr3 | GO:0005759 | Not Cancer Driver | No | 38 | 0.187 | 12 | 1 | 0.083 | 0 |
| GRPEL1 | GRPEL1 | Q9HAV7 | GrpE protein homolog 1, mitochondrial | chr4 | GO:0005759 | Not Cancer Driver | No | 22 | 0.101 | 88 | 7 | 0.08 | 0 |
| GSR | GSR | P00390 | Glutathione reductase, mitochondrial | chr8 | GO:0005759 | Not Cancer Driver | No | 53 | 0.102 | 55 | 5 | 0.091 | 1 |
| GSTK1_ENST00000358406 | GSTK1 | Q9Y2Q3 | Glutathione S-transferase kappa 1 | chr7 | GO:0005759 | Not Cancer Driver | No | 33 | 0.146 | 30 | 3 | 0.1 | 0 |
| GSTZ1 | GSTZ1 | O43708 | Maleylacetoacetate isomerase | chr14 | GO:0005759 | Not Cancer Driver | No | 30 | 0.139 | 19 | 2 | 0.105 | 2 |
| GUF1 | GUF1 | Q8N442 | Translation factor GUF1, mitochondrial | chr4 | GO:0005759 | Not Cancer Driver | No | 75 | 0.112 | 38 | 5 | 0.132 | 1 |
| HADH_ENST00000309522 | HADH | Q16836 | Hydroxyacyl-coenzyme A dehydrogenase, mitochondrial | chr4 | GO:0005759 | Not Cancer Driver | No | 33 | 0.105 | 22 | 5 | 0.227 | 3 |
| HAGH | HAGH | Q16775 | Hydroxyacylglutathione hydrolase, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 26 | 0.084 | 41 | 1 | 0.024 | 0 |
| HARS2_ENST00000642231 | HARS2 | P49590 | Histidine--tRNA ligase, mitochondrial | chr5 | GO:0005759 | Not Cancer Driver | No | 48 | 0.095 | 34 | 4 | 0.118 | 2 |
| HIBADH | HIBADH | P31937 | 3-hydroxyisobutyrate dehydrogenase, mitochondrial | chr7 | GO:0005759 | Not Cancer Driver | No | 28 | 0.083 | 7 | 2 | 0.286 | 0 |
| HIBCH | HIBCH | Q6NVY1 | 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 42 | 0.109 | 26 | 0 | 0.0 | 1 |
| HMGCL | HMGCL | P35914 | Hydroxymethylglutaryl-CoA lyase, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 17 | 0.052 | 8 | 2 | 0.25 | 19 |
| HMGCS2 | HMGCS2 | P54868 | Hydroxymethylglutaryl-CoA synthase, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 92 | 0.181 | 29 | 4 | 0.138 | 19 |
| HOGA1 | HOGA1 | Q86XE5 | 4-hydroxy-2-oxoglutarate aldolase, mitochondrial | chr10 | GO:0005759 | Not Cancer Driver | No | 34 | 0.104 | 2 | 0 | 0.0 | 2 |
| HSD17B10 | HSD17B10 | Q99714 | 3-hydroxyacyl-CoA dehydrogenase type-2 | chrX | GO:0005759 | Not Cancer Driver | No | 27 | 0.103 | 15 | 3 | 0.2 | 11 |
| HSD17B8 | HSD17B8 | Q92506 | (3R)-3-hydroxyacyl-CoA dehydrogenase | chr6 | GO:0005759 | Not Cancer Driver | No | 20 | 0.077 | 26 | 1 | 0.038 | 0 |
| HSPA1L | HSPA1L | P34931 | Heat shock 70 kDa protein 1-like | chr6 | GO:0005759 | Not Cancer Driver | No | 119 | 0.186 | 141 | 28 | 0.199 | 0 |
| HSPA9 | HSPA9 | P38646 | Stress-70 protein, mitochondrial | chr5 | GO:0005759 | Not Cancer Driver | No | 67 | 0.099 | 283 | 26 | 0.092 | 2 |
| HSPD1 | HSPD1 | P10809 | 60 kDa heat shock protein, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 61 | 0.106 | 82 | 6 | 0.073 | 2 |
| HSPE1 | HSPE1 | P61604 | 10 kDa heat shock protein, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 8 | 0.078 | 3 | 0 | 0.0 | 0 |
| HTD2_ENST00000461393 | HTD2 | P86397 | Hydroxyacyl-thioester dehydratase type 2, mitochondrial | chr3 | GO:0005759 | Not Cancer Driver | No | 1 | 0.006 | 0 | 0 | 0.0 | 0 |
| HYKK_ENST00000388988 | HYKK | A2RU49 | Hydroxylysine kinase | chr15 | GO:0005759 | Not Cancer Driver | No | 38 | 0.102 | 30 | 3 | 0.1 | 0 |
| IARS2 | IARS2 | Q9NSE4 | Isoleucine--tRNA ligase, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 149 | 0.147 | 145 | 22 | 0.152 | 0 |
| IBA57 | IBA57 | Q5T440 | Putative transferase CAF17, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 39 | 0.11 | 28 | 1 | 0.036 | 1 |
| IDH2 | IDH2 | P48735 | Isocitrate dehydrogenase [NADP], mitochondrial | chr15 | GO:0005759 | Census, Compendium | Yes | 74 | 0.164 | 59 | 1 | 0.017 | 7 |
| IDH3A | IDH3A | P50213 | Isocitrate dehydrogenase [NAD] subunit alpha, mitochondrial | chr15 | GO:0005759 | Not Cancer Driver | No | 41 | 0.112 | 47 | 11 | 0.234 | 0 |
| IDH3B_ENST00000380843 | IDH3B | O43837 | Isocitrate dehydrogenase [NAD] subunit beta, mitochondrial | chr20 | GO:0005759 | Not Cancer Driver | No | 32 | 0.083 | 49 | 3 | 0.061 | 1 |
| IDH3G | IDH3G | P51553 | Isocitrate dehydrogenase [NAD] subunit gamma, mitochondrial | chrX | GO:0005759 | Not Cancer Driver | No | 48 | 0.122 | 77 | 9 | 0.117 | 0 |
| ISCA1 | ISCA1 | Q9BUE6 | Iron-sulfur cluster assembly 1 homolog, mitochondrial | chr9 | GO:0005759 | Not Cancer Driver | No | 8 | 0.062 | 11 | 1 | 0.091 | 0 |
| ISCA2 | ISCA2 | Q86U28 | Iron-sulfur cluster assembly 2 homolog, mitochondrial | chr14 | GO:0005759 | Not Cancer Driver | No | 13 | 0.084 | 38 | 3 | 0.079 | 1 |
| ISCU | ISCU | Q9H1K1 | Iron-sulfur cluster assembly enzyme ISCU, mitochondrial | chr12 | GO:0005759 | Not Cancer Driver | No | 14 | 0.084 | 24 | 3 | 0.125 | 0 |
| IVD | IVD | P26440 | Isovaleryl-CoA dehydrogenase, mitochondrial | chr15 | GO:0005759 | Not Cancer Driver | No | 46 | 0.108 | 8 | 0 | 0.0 | 14 |
| KARS_ENST00000302445 | KARS1 | Q15046 | Lysine--tRNA ligase | chr16 | GO:0005759 | Not Cancer Driver | No | 88 | 0.147 | 160 | 15 | 0.094 | 12 |
| KIAA0391 | PRORP | O15091 | Mitochondrial ribonuclease P catalytic subunit | chr14 | GO:0005759 | Not Cancer Driver | No | 62 | 0.106 | 60 | 12 | 0.2 | 0 |
| LACTB2 | LACTB2 | Q53H82 | Endoribonuclease LACTB2 | chr8 | GO:0005759 | Not Cancer Driver | No | 34 | 0.118 | 21 | 1 | 0.048 | 0 |
| LARS2_ENST00000645846 | LARS2 | Q15031 | Leucine--tRNA ligase, mitochondrial | chr3 | GO:0005759 | Not Cancer Driver | No | 74 | 0.082 | 80 | 8 | 0.1 | 3 |
| LDHAL6B | LDHAL6B | Q9BYZ2 | L-lactate dehydrogenase A-like 6B | chr15 | GO:0005759 | Not Cancer Driver | No | 54 | 0.142 | 17 | 2 | 0.118 | 0 |
| LIAS | LIAS | O43766 | Lipoyl synthase, mitochondrial | chr4 | GO:0005759 | Not Cancer Driver | No | 46 | 0.124 | 82 | 10 | 0.122 | 1 |
| LIPT1 | LIPT1 | Q9Y234 | Lipoyltransferase 1, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 34 | 0.091 | 0 | 0 | 0.0 | 3 |
| LIPT2 | LIPT2 | A6NK58 | Putative lipoyltransferase 2, mitochondrial | chr11 | GO:0005759 | Not Cancer Driver | No | 4 | 0.017 | 14 | 0 | 0.0 | 3 |
| LONP1 | LONP1 | P36776 | Lon protease homolog, mitochondrial | chr19 | GO:0005759 | Not Cancer Driver | No | 99 | 0.103 | 175 | 15 | 0.086 | 10 |
| LRRK2 | LRRK2 | Q5S007 | Leucine-rich repeat serine/threonine-protein kinase 2 | chr12 | GO:0005759 | Not Cancer Driver | No | 519 | 0.205 | 90 | 17 | 0.189 | 23 |
| LYRM4_ENST00000330636 | LYRM4 | Q9HD34 | LYR motif-containing protein 4 | chr6 | GO:0005759 | Not Cancer Driver | No | 14 | 0.154 | 11 | 1 | 0.091 | 1 |
| LYRM7 | LYRM7 | Q5U5X0 | Complex III assembly factor LYRM7 | chr5 | GO:0005759 | Not Cancer Driver | No | 5 | 0.048 | 28 | 1 | 0.036 | 1 |
| MAIP1 | MAIP1 | Q8WWC4 | m-AAA protease-interacting protein 1, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 28 | 0.096 | 12 | 0 | 0.0 | 0 |
| MARS2 | MARS2 | Q96GW9 | Methionine--tRNA ligase, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 75 | 0.126 | 34 | 6 | 0.176 | 1 |
| MCAT | MCAT | Q8IVS2 | Malonyl-CoA-acyl carrier protein transacylase, mitochondrial | chr22 | GO:0005759 | Not Cancer Driver | No | 38 | 0.097 | 52 | 2 | 0.038 | 0 |
| MCCC1 | MCCC1 | Q96RQ3 | Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial | chr3 | GO:0005759 | Not Cancer Driver | No | 94 | 0.13 | 162 | 17 | 0.105 | 33 |
| MCCC2 | MCCC2 | Q9HCC0 | Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial | chr5 | GO:0005759 | Not Cancer Driver | No | 60 | 0.107 | 25 | 2 | 0.08 | 52 |
| MCEE | MCEE | Q96PE7 | Methylmalonyl-CoA epimerase, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 19 | 0.108 | 9 | 0 | 0.0 | 0 |
| MDH2 | MDH2 | P40926 | Malate dehydrogenase, mitochondrial | chr7 | GO:0005759 | Not Cancer Driver | No | 39 | 0.115 | 8 | 1 | 0.125 | 3 |
| ME2 | ME2 | P23368 | NAD-dependent malic enzyme, mitochondrial | chr18 | GO:0005759 | Not Cancer Driver | No | 69 | 0.118 | 32 | 5 | 0.156 | 0 |
| ME3_ENST00000393324 | ME3 | Q16798 | NADP-dependent malic enzyme, mitochondrial | chr11 | GO:0005759 | Not Cancer Driver | No | 105 | 0.174 | 45 | 9 | 0.2 | 0 |
| MECR | MECR | Q9BV79 | Enoyl-[acyl-carrier-protein] reductase, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 55 | 0.147 | 26 | 5 | 0.192 | 3 |
| METTL15 | METTL15 | A6NJ78 | 12S rRNA N4-methylcytidine (m4C) methyltransferase | chr11 | GO:0005759 | Not Cancer Driver | No | 46 | 0.113 | 92 | 14 | 0.152 | 0 |
| METTL17_ENST00000339374 | METTL17 | Q9H7H0 | Methyltransferase-like protein 17, mitochondrial | chr14 | GO:0005759 | Not Cancer Driver | No | 62 | 0.136 | 95 | 16 | 0.168 | 0 |
| METTL4 | METTL4 | Q8N3J2 | N(6)-adenine-specific methyltransferase METTL4 | chr18 | GO:0005759 | Not Cancer Driver | No | 61 | 0.129 | 34 | 4 | 0.118 | 0 |
| MIPEP | MIPEP | Q99797 | Mitochondrial intermediate peptidase | chr13 | GO:0005759 | Not Cancer Driver | No | 77 | 0.108 | 40 | 2 | 0.05 | 3 |
| MLYCD | MLYCD | O95822 | Malonyl-CoA decarboxylase, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 41 | 0.083 | 82 | 0 | 0.0 | 0 |
| MMAA | MMAA | Q8IVH4 | Methylmalonic aciduria type A protein, mitochondrial | chr4 | GO:0005759 | Not Cancer Driver | No | 58 | 0.139 | 46 | 6 | 0.13 | 22 |
| MMAB | MMAB | Q96EY8 | Corrinoid adenosyltransferase MMAB | chr12 | GO:0005759 | Not Cancer Driver | No | 36 | 0.144 | 68 | 14 | 0.206 | 5 |
| MMUT | MMUT | P22033 | Methylmalonyl-CoA mutase, mitochondrial | chr6 | GO:0005759 | Not Cancer Driver | No | 107 | 0.143 | 99 | 11 | 0.111 | 125 |
| MPST_ENST00000341116 | MPST | P25325 | 3-mercaptopyruvate sulfurtransferase | chr22 | GO:0005759 | Not Cancer Driver | No | 20 | 0.067 | 72 | 8 | 0.111 | 0 |
| MRM2_ENST00000440306 | MRM2 | Q9UI43 | rRNA methyltransferase 2, mitochondrial | chr7 | GO:0005759 | Not Cancer Driver | No | 37 | 0.15 | 15 | 1 | 0.067 | 1 |
| MRM3 | MRM3 | Q9HC36 | rRNA methyltransferase 3, mitochondrial | chr17 | GO:0005759 | Not Cancer Driver | No | 45 | 0.107 | 83 | 8 | 0.096 | 0 |
| MRPL58 | MRPL58 | Q14197 | Peptidyl-tRNA hydrolase ICT1, mitochondrial | chr17 | GO:0005759 | Not Cancer Driver | No | 28 | 0.136 | 105 | 13 | 0.124 | 0 |
| MRRF | MRRF | Q96E11 | Ribosome-recycling factor, mitochondrial | chr9 | GO:0005759 | Not Cancer Driver | No | 23 | 0.088 | 118 | 9 | 0.076 | 0 |
| MTERF1 | MTERF1 | Q99551 | Transcription termination factor 1, mitochondrial | chr7 | GO:0005759 | Not Cancer Driver | No | 48 | 0.12 | 0 | 0 | 0.0 | 0 |
| MTERF2 | MTERF2 | Q49AM1 | Transcription termination factor 2, mitochondrial | chr12 | GO:0005759 | Not Cancer Driver | No | 49 | 0.127 | 0 | 0 | 0.0 | 0 |
| MTERF4 | MTERF4 | Q7Z6M4 | Transcription termination factor 4, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 47 | 0.123 | 100 | 11 | 0.11 | 0 |
| MTG1 | MTG1 | Q9BT17 | Mitochondrial ribosome-associated GTPase 1 | chr10 | GO:0005759 | Not Cancer Driver | No | 43 | 0.129 | 16 | 3 | 0.188 | 0 |
| MTG2 | MTG2 | Q9H4K7 | Mitochondrial ribosome-associated GTPase 2 | chr20 | GO:0005759 | Not Cancer Driver | No | 57 | 0.14 | 47 | 9 | 0.191 | 0 |
| MTHFD1L_ENST00000367321 | MTHFD1L | Q6UB35 | Monofunctional C1-tetrahydrofolate synthase, mitochondrial | chr6 | GO:0005759 | Not Cancer Driver | No | 117 | 0.12 | 139 | 11 | 0.079 | 0 |
| MTHFD2 | MTHFD2 | P13995 | Bifunctional methylenetetrahydrofolate dehydrogenase/cyclohydrolase, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 39 | 0.111 | 39 | 3 | 0.077 | 0 |
| MTHFD2L | MTHFD2L | Q9H903 | Bifunctional methylenetetrahydrofolate dehydrogenase/cyclohydrolase 2, mitochondrial | chr4 | GO:0005759 | Not Cancer Driver | No | 45 | 0.13 | 59 | 6 | 0.102 | 0 |
| MTHFS | MTHFS | P49914 | 5-formyltetrahydrofolate cyclo-ligase | chr15 | GO:0005759 | Not Cancer Driver | No | 18 | 0.089 | 36 | 6 | 0.167 | 2 |
| MTRF1L | MTRF1L | Q9UGC7 | Peptide chain release factor 1-like, mitochondrial | chr6 | GO:0005759 | Not Cancer Driver | No | 31 | 0.082 | 183 | 12 | 0.066 | 0 |
| NADK2 | NADK2 | Q4G0N4 | NAD kinase 2, mitochondrial | chr5 | GO:0005759 | Not Cancer Driver | No | 42 | 0.095 | 89 | 3 | 0.034 | 0 |
| NAGS | NAGS | Q8N159 | N-acetylglutamate synthase, mitochondrial | chr17 | GO:0005759 | Not Cancer Driver | No | 35 | 0.066 | 116 | 6 | 0.052 | 6 |
| NARS2 | NARS2 | Q96I59 | Probable asparagine--tRNA ligase, mitochondrial | chr11 | GO:0005759 | Not Cancer Driver | No | 79 | 0.166 | 22 | 2 | 0.091 | 3 |
| NAT8L | NAT8L | Q8N9F0 | N-acetylaspartate synthetase | chr4 | GO:0005759 | Not Cancer Driver | No | 20 | 0.066 | 57 | 0 | 0.0 | 0 |
| NAXE | NAXE | Q8NCW5 | NAD(P)H-hydrate epimerase | chr1 | GO:0005759 | Not Cancer Driver | No | 22 | 0.076 | 5 | 0 | 0.0 | 2 |
| NDUFA10 | NDUFA10 | O95299 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 10, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 48 | 0.135 | 19 | 0 | 0.0 | 1 |
| NDUFA9 | NDUFA9 | Q16795 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 9, mitochondrial | chr12 | GO:0005759 | Not Cancer Driver | No | 57 | 0.151 | 8 | 0 | 0.0 | 2 |
| NDUFAB1_ENST00000007516 | NDUFAB1 | O14561 | Acyl carrier protein, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 23 | 0.147 | 0 | 0 | 0.0 | 0 |
| NDUFAF1 | NDUFAF1 | Q9Y375 | Complex I intermediate-associated protein 30, mitochondrial | chr15 | GO:0005759 | Not Cancer Driver | No | 44 | 0.135 | 63 | 8 | 0.127 | 4 |
| NDUFAF7 | NDUFAF7 | Q7L592 | Protein arginine methyltransferase NDUFAF7, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 53 | 0.12 | 19 | 3 | 0.158 | 0 |
| NDUFB8 | NDUFB8 | O95169 | NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 8, mitochondrial | chr10 | GO:0005759 | Not Cancer Driver | No | 28 | 0.151 | 64 | 11 | 0.172 | 3 |
| NDUFS1_ENST00000449699 | NDUFS1 | P28331 | NADH-ubiquinone oxidoreductase 75 kDa subunit, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 81 | 0.111 | 40 | 3 | 0.075 | 2 |
| NDUFS2 | NDUFS2 | O75306 | NADH dehydrogenase [ubiquinone] iron-sulfur protein 2, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 58 | 0.125 | 49 | 5 | 0.102 | 4 |
| NDUFS3 | NDUFS3 | O75489 | NADH dehydrogenase [ubiquinone] iron-sulfur protein 3, mitochondrial | chr11 | GO:0005759 | Not Cancer Driver | No | 34 | 0.129 | 26 | 3 | 0.115 | 2 |
| NDUFS7 | NDUFS7 | O75251 | NADH dehydrogenase [ubiquinone] iron-sulfur protein 7, mitochondrial | chr19 | GO:0005759 | Not Cancer Driver | No | 36 | 0.169 | 30 | 3 | 0.1 | 1 |
| NDUFS8 | NDUFS8 | O00217 | NADH dehydrogenase [ubiquinone] iron-sulfur protein 8, mitochondrial | chr11 | GO:0005759 | Not Cancer Driver | No | 27 | 0.129 | 37 | 2 | 0.054 | 3 |
| NFS1 | NFS1 | Q9Y697 | Cysteine desulfurase, mitochondrial | chr20 | GO:0005759 | Not Cancer Driver | No | 46 | 0.101 | 72 | 9 | 0.125 | 1 |
| NME4 | NME4 | O00746 | Nucleoside diphosphate kinase, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 13 | 0.07 | 41 | 4 | 0.098 | 0 |
| NMNAT3 | NMNAT3 | Q96T66 | Nicotinamide/nicotinic acid mononucleotide adenylyltransferase 3 | chr3 | GO:0005759 | Not Cancer Driver | No | 32 | 0.127 | 53 | 6 | 0.113 | 0 |
| NR3C1_ENST00000343796 | NR3C1 | P04150 | Glucocorticoid receptor | chr5 | GO:0005759 | Not Cancer Driver | No | 92 | 0.118 | 362 | 37 | 0.102 | 12 |
| NSUN3 | NSUN3 | Q9H649 | tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial | chr3 | GO:0005759 | Not Cancer Driver | No | 34 | 0.1 | 0 | 0 | 0.0 | 0 |
| NSUN4 | NSUN4 | Q96CB9 | 5-methylcytosine rRNA methyltransferase NSUN4 | chr1 | GO:0005759 | Not Cancer Driver | No | 40 | 0.104 | 20 | 5 | 0.25 | 0 |
| NT5M | NT5M | Q9NPB1 | 5'(3')-deoxyribonucleotidase, mitochondrial | chr17 | GO:0005759 | Not Cancer Driver | No | 20 | 0.088 | 0 | 0 | 0.0 | 0 |
| NUBPL | NUBPL | Q8TB37 | Iron-sulfur protein NUBPL | chr14 | GO:0005759 | Not Cancer Driver | No | 32 | 0.1 | 49 | 1 | 0.02 | 2 |
| NUDT13 | NUDT13 | Q86X67 | NAD(P)H pyrophosphatase NUDT13, mitochondrial | chr10 | GO:0005759 | Not Cancer Driver | No | 40 | 0.114 | 19 | 0 | 0.0 | 0 |
| NUDT1_ENST00000397046 | NUDT1 | P36639 | Oxidized purine nucleoside triphosphate hydrolase | chr7 | GO:0005759 | Not Cancer Driver | No | 25 | 0.16 | 17 | 4 | 0.235 | 0 |
| NUDT2_ENST00000346365 | NUDT2 | P50583 | Bis(5'-nucleosyl)-tetraphosphatase [asymmetrical] | chr9 | GO:0005759 | Not Cancer Driver | No | 16 | 0.109 | 24 | 1 | 0.042 | 0 |
| NUDT9 | NUDT9 | Q9BW91 | ADP-ribose pyrophosphatase, mitochondrial | chr4 | GO:0005759 | Not Cancer Driver | No | 27 | 0.077 | 177 | 16 | 0.09 | 0 |
| OAT | OAT | P04181 | Ornithine aminotransferase, mitochondrial | chr10 | GO:0005759 | Not Cancer Driver | No | 52 | 0.118 | 17 | 0 | 0.0 | 27 |
| OGDH | OGDH | Q02218 | 2-oxoglutarate dehydrogenase complex component E1 | chr7 | GO:0005759 | Not Cancer Driver | No | 150 | 0.147 | 106 | 19 | 0.179 | 0 |
| OGDHL | OGDHL | Q9ULD0 | 2-oxoglutarate dehydrogenase-like, mitochondrial | chr10 | GO:0005759 | Not Cancer Driver | No | 262 | 0.259 | 128 | 38 | 0.297 | 0 |
| OGG1_ENST00000344629 | OGG1 | O15527 | N-glycosylase/DNA lyase | chr3 | GO:0005759 | Not Cancer Driver | No | 37 | 0.107 | 71 | 12 | 0.169 | 0 |
| OTC | OTC | P00480 | Ornithine transcarbamylase, mitochondrial | chrX | GO:0005759 | Not Cancer Driver | No | 89 | 0.251 | 24 | 4 | 0.167 | 111 |
| OXA1L_ENST00000604262 | OXA1L | Q15070 | Mitochondrial inner membrane protein OXA1L | chr14 | GO:0005759 | Not Cancer Driver | No | 36 | 0.083 | 81 | 9 | 0.111 | 0 |
| OXCT1 | OXCT1 | P55809 | Succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial | chr5 | GO:0005759 | Not Cancer Driver | No | 80 | 0.154 | 39 | 5 | 0.128 | 11 |
| OXCT2 | OXCT2 | Q9BYC2 | Succinyl-CoA:3-ketoacid coenzyme A transferase 2, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 55 | 0.106 | 56 | 6 | 0.107 | 0 |
| PABPC5 | PABPC5 | Q96DU9 | Polyadenylate-binding protein 5 | chrX | GO:0005759 | Not Cancer Driver | No | 132 | 0.346 | 26 | 9 | 0.346 | 0 |
| PAM16_ENST00000576217 | PAM16 | Q9Y3D7 | Mitochondrial import inner membrane translocase subunit TIM16 | chr16 | GO:0005759 | Not Cancer Driver | No | 23 | 0.184 | 49 | 11 | 0.224 | 1 |
| PARG_ENST00000616448 | PARG | Q86W56 | Poly(ADP-ribose) glycohydrolase | chr10 | GO:0005759 | Not Cancer Driver | No | 60 | 0.061 | 519 | 1 | 0.002 | 0 |
| PARK7_ENST00000377488 | PARK7 | Q99497 | Parkinson disease protein 7 | chr1 | GO:0005759 | Not Cancer Driver | No | 11 | 0.058 | 30 | 0 | 0.0 | 5 |
| PARS2 | PARS2 | Q7L3T8 | Probable proline--tRNA ligase, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 50 | 0.105 | 8 | 2 | 0.25 | 0 |
| PC | PC | P11498 | Pyruvate carboxylase, mitochondrial | chr11 | GO:0005759 | Not Cancer Driver | No | 185 | 0.157 | 172 | 27 | 0.157 | 9 |
| PCCA | PCCA | P05165 | Propionyl-CoA carboxylase alpha chain, mitochondrial | chr13 | GO:0005759 | Not Cancer Driver | No | 102 | 0.14 | 42 | 14 | 0.333 | 16 |
| PCCB_ENST00000251654 | PCCB | P05166 | Propionyl-CoA carboxylase beta chain, mitochondrial | chr3 | GO:0005759 | Not Cancer Driver | No | 59 | 0.109 | 64 | 12 | 0.188 | 25 |
| PCK2 | PCK2 | Q16822 | Phosphoenolpyruvate carboxykinase [GTP], mitochondrial | chr14 | GO:0005759 | Not Cancer Driver | No | 91 | 0.142 | 139 | 13 | 0.094 | 0 |
| PDE12 | PDE12 | Q6L8Q7 | 2',5'-phosphodiesterase 12 | chr3 | GO:0005759 | Not Cancer Driver | No | 59 | 0.097 | 129 | 8 | 0.062 | 0 |
| PDE2A | PDE2A | O00408 | cGMP-dependent 3',5'-cyclic phosphodiesterase | chr11 | GO:0005759 | Not Cancer Driver | No | 137 | 0.146 | 99 | 7 | 0.071 | 0 |
| PDHA1_ENST00000422285 | PDHA1 | P08559 | Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial | chrX | GO:0005759 | Not Cancer Driver | No | 70 | 0.179 | 43 | 6 | 0.14 | 20 |
| PDHA2 | PDHA2 | P29803 | Pyruvate dehydrogenase E1 component subunit alpha, testis-specific form, mitochondrial | chr4 | GO:0005759 | Not Cancer Driver | No | 163 | 0.42 | 41 | 17 | 0.415 | 0 |
| PDHB | PDHB | P11177 | Pyruvate dehydrogenase E1 component subunit beta, mitochondrial | chr3 | GO:0005759 | Not Cancer Driver | No | 32 | 0.089 | 4 | 0 | 0.0 | 2 |
| PDHX | PDHX | O00330 | Pyruvate dehydrogenase protein X component, mitochondrial | chr11 | GO:0005759 | Not Cancer Driver | No | 62 | 0.124 | 179 | 28 | 0.156 | 0 |
| PDK1_ENST00000282077 | PDK1 | Q15118 | [Pyruvate dehydrogenase (acetyl-transferring)] kinase isozyme 1, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 52 | 0.119 | 50 | 10 | 0.2 | 0 |
| PDK2 | PDK2 | Q15119 | [Pyruvate dehydrogenase (acetyl-transferring)] kinase isozyme 2, mitochondrial | chr17 | GO:0005759 | Not Cancer Driver | No | 45 | 0.111 | 35 | 4 | 0.114 | 0 |
| PDK3_ENST00000379162 | PDK3 | Q15120 | [Pyruvate dehydrogenase (acetyl-transferring)] kinase isozyme 3, mitochondrial | chrX | GO:0005759 | Not Cancer Driver | No | 61 | 0.15 | 28 | 6 | 0.214 | 1 |
| PDK4 | PDK4 | Q16654 | [Pyruvate dehydrogenase (acetyl-transferring)] kinase isozyme 4, mitochondrial | chr7 | GO:0005759 | Not Cancer Driver | No | 70 | 0.17 | 14 | 2 | 0.143 | 0 |
| PDP1_ENST00000297598 | PDP1 | Q9P0J1 | [Pyruvate dehydrogenase [acetyl-transferring]]-phosphatase 1, mitochondrial | chr8 | GO:0005759 | Not Cancer Driver | No | 64 | 0.119 | 96 | 9 | 0.094 | 0 |
| PDP2 | PDP2 | Q9P2J9 | [Pyruvate dehydrogenase [acetyl-transferring]]-phosphatase 2, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 52 | 0.098 | 51 | 11 | 0.216 | 0 |
| PDPR | PDPR | Q8NCN5 | Pyruvate dehydrogenase phosphatase regulatory subunit, mitochondrial | chr16 | GO:0005759 | Compendium | Yes | 142 | 0.162 | 35 | 4 | 0.114 | 0 |
| PDSS1 | PDSS1 | Q5T2R2 | All trans-polyprenyl-diphosphate synthase PDSS1 | chr10 | GO:0005759 | Not Cancer Driver | No | 50 | 0.12 | 51 | 5 | 0.098 | 1 |
| PDSS2 | PDSS2 | Q86YH6 | All trans-polyprenyl-diphosphate synthase PDSS2 | chr6 | GO:0005759 | Not Cancer Driver | No | 39 | 0.098 | 7 | 0 | 0.0 | 1 |
| PHYKPL | PHYKPL | Q8IUZ5 | 5-phosphohydroxy-L-lysine phospho-lyase | chr5 | GO:0005759 | Not Cancer Driver | No | 50 | 0.111 | 33 | 5 | 0.152 | 2 |
| PITRM1_ENST00000224949 | PITRM1 | Q5JRX3 | Presequence protease, mitochondrial | chr10 | GO:0005759 | Not Cancer Driver | No | 122 | 0.118 | 220 | 26 | 0.118 | 2 |
| PNPT1 | PNPT1 | Q8TCS8 | Polyribonucleotide nucleotidyltransferase 1, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 86 | 0.11 | 115 | 10 | 0.087 | 2 |
| POLDIP2 | POLDIP2 | Q9Y2S7 | Polymerase delta-interacting protein 2 | chr17 | GO:0005759 | Not Cancer Driver | No | 36 | 0.098 | 94 | 13 | 0.138 | 0 |
| POLG2 | POLG2 | Q9UHN1 | DNA polymerase subunit gamma-2, mitochondrial | chr17 | GO:0005759 | Not Cancer Driver | No | 64 | 0.132 | 46 | 4 | 0.087 | 3 |
| POLG_ENST00000442287 | POLG | P54098 | DNA polymerase subunit gamma-1 | chr15 | GO:0005759 | Census | Yes | 139 | 0.112 | 421 | 42 | 0.1 | 73 |
| POLRMT | POLRMT | O00411 | DNA-directed RNA polymerase, mitochondrial | chr19 | GO:0005759 | Not Cancer Driver | No | 188 | 0.153 | 253 | 31 | 0.123 | 0 |
| PPA2 | PPA2 | Q9H2U2 | Inorganic pyrophosphatase 2, mitochondrial | chr4 | GO:0005759 | Not Cancer Driver | No | 49 | 0.147 | 71 | 9 | 0.127 | 9 |
| PPIF | PPIF | P30405 | Peptidyl-prolyl cis-trans isomerase F, mitochondrial | chr10 | GO:0005759 | Not Cancer Driver | No | 19 | 0.092 | 43 | 4 | 0.093 | 0 |
| PPM1K | PPM1K | Q8N3J5 | Protein phosphatase 1K, mitochondrial | chr4 | GO:0005759 | Not Cancer Driver | No | 59 | 0.159 | 62 | 12 | 0.194 | 0 |
| PPTC7 | PPTC7 | Q8NI37 | Protein phosphatase PTC7 homolog | chr12 | GO:0005759 | Not Cancer Driver | No | 32 | 0.105 | 36 | 2 | 0.056 | 0 |
| PRDX3 | PRDX3 | P30048 | Thioredoxin-dependent peroxide reductase, mitochondrial | chr10 | GO:0005759 | Not Cancer Driver | No | 23 | 0.09 | 23 | 3 | 0.13 | 0 |
| PRDX5 | PRDX5 | P30044 | Peroxiredoxin-5, mitochondrial | chr11 | GO:0005759 | Not Cancer Driver | No | 22 | 0.103 | 0 | 0 | 0.0 | 0 |
| PRIMPOL_ENST00000503752 | PRIMPOL | Q96LW4 | DNA-directed primase/polymerase protein | chr4 | GO:0005759 | Not Cancer Driver | No | 50 | 0.089 | 92 | 7 | 0.076 | 0 |
| PRODH_ENST00000610940 | PRODH | O43272 | Proline dehydrogenase 1, mitochondrial | chr22 | GO:0005759 | Not Cancer Driver | No | 62 | 0.103 | 67 | 8 | 0.119 | 16 |
| PTCD1 | PTCD1 | O75127 | Pentatricopeptide repeat-containing protein 1, mitochondrial | chr7 | GO:0005759 | Not Cancer Driver | No | 99 | 0.141 | 224 | 42 | 0.188 | 0 |
| PTPN1 | PTPN1 | P18031 | Tyrosine-protein phosphatase non-receptor type 1 | chr20 | GO:0005759 | Not Cancer Driver | No | 49 | 0.113 | 140 | 25 | 0.179 | 0 |
| PUS1 | PUS1 | Q9Y606 | Pseudouridylate synthase 1 homolog | chr12 | GO:0005759 | Not Cancer Driver | No | 48 | 0.112 | 157 | 18 | 0.115 | 1 |
| PYCR1_ENST00000329875 | PYCR1 | P32322 | Pyrroline-5-carboxylate reductase 1, mitochondrial | chr17 | GO:0005759 | Not Cancer Driver | No | 31 | 0.097 | 67 | 10 | 0.149 | 9 |
| PYCR2 | PYCR2 | Q96C36 | Pyrroline-5-carboxylate reductase 2 | chr1 | GO:0005759 | Not Cancer Driver | No | 31 | 0.097 | 41 | 3 | 0.073 | 2 |
| PYROXD2 | PYROXD2 | Q8N2H3 | Pyridine nucleotide-disulfide oxidoreductase domain-containing protein 2 | chr10 | GO:0005759 | Not Cancer Driver | No | 60 | 0.103 | 34 | 1 | 0.029 | 0 |
| QARS | QARS1 | P47897 | Glutamine--tRNA ligase | chr3 | GO:0005759 | Not Cancer Driver | No | 101 | 0.13 | 106 | 16 | 0.151 | 4 |
| RAD51_ENST00000267868 | RAD51 | Q06609 | DNA repair protein RAD51 homolog 1 | chr15 | GO:0005759 | Not Cancer Driver | No | 42 | 0.124 | 47 | 5 | 0.106 | 3 |
| RARS2 | RARS2 | Q5T160 | Probable arginine--tRNA ligase, mitochondrial | chr6 | GO:0005759 | Not Cancer Driver | No | 88 | 0.152 | 20 | 1 | 0.05 | 0 |
| REXO2 | REXO2 | Q9Y3B8 | Oligoribonuclease, mitochondrial | chr11 | GO:0005759 | Not Cancer Driver | No | 19 | 0.08 | 43 | 4 | 0.093 | 0 |
| RIDA | RIDA | P52758 | 2-iminobutanoate/2-iminopropanoate deaminase | chr8 | GO:0005759 | Not Cancer Driver | No | 20 | 0.146 | 3 | 0 | 0.0 | 0 |
| RNASEL | RNASEL | Q05823 | 2-5A-dependent ribonuclease | chr1 | GO:0005759 | Not Cancer Driver | No | 95 | 0.128 | 147 | 17 | 0.116 | 0 |
| RPS3_ENST00000527446 | RPS3 | P23396 | 40S ribosomal protein S3 | chr11 | GO:0005759 | Not Cancer Driver | No | 22 | 0.091 | 48 | 4 | 0.083 | 0 |
| RPUSD3 | RPUSD3 | Q6P087 | Mitochondrial mRNA pseudouridine synthase RPUSD3 | chr3 | GO:0005759 | Not Cancer Driver | No | 33 | 0.094 | 85 | 5 | 0.059 | 0 |
| RPUSD4 | RPUSD4 | Q96CM3 | Pseudouridylate synthase RPUSD4, mitochondrial | chr11 | GO:0005759 | Not Cancer Driver | No | 54 | 0.143 | 97 | 15 | 0.155 | 0 |
| SARDH_ENST00000439388 | SARDH | Q9UL12 | Sarcosine dehydrogenase, mitochondrial | chr9 | GO:0005759 | Not Cancer Driver | No | 144 | 0.157 | 132 | 24 | 0.182 | 2 |
| SARS2_ENST00000221431 | SARS2 | Q9NP81 | Serine--tRNA ligase, mitochondrial | chr19 | GO:0005759 | Not Cancer Driver | No | 64 | 0.124 | 111 | 14 | 0.126 | 1 |
| SCO2_ENST00000395693 | SCO2 | O43819 | Protein SCO2 homolog, mitochondrial | chr22 | GO:0005759 | Not Cancer Driver | No | 31 | 0.117 | 51 | 8 | 0.157 | 8 |
| SDHAF1 | SDHAF1 | A6NFY7 | Succinate dehydrogenase assembly factor 1, mitochondrial | chr19 | GO:0005759 | Not Cancer Driver | No | 1 | 0.009 | 108 | 1 | 0.009 | 3 |
| SDHAF2 | SDHAF2 | Q9NX18 | Succinate dehydrogenase assembly factor 2, mitochondrial | chr11 | GO:0005759 | Census | Yes | 29 | 0.175 | 22 | 5 | 0.227 | 1 |
| SDHAF3 | SDHAF3 | Q9NRP4 | Succinate dehydrogenase assembly factor 3, mitochondrial | chr7 | GO:0005759 | Not Cancer Driver | No | 18 | 0.144 | 65 | 5 | 0.077 | 0 |
| SDHAF4 | SDHAF4 | Q5VUM1 | Succinate dehydrogenase assembly factor 4, mitochondrial | chr6 | GO:0005759 | Not Cancer Driver | No | 14 | 0.13 | 76 | 10 | 0.132 | 0 |
| SHC1_ENST00000368445 | SHC1 | P29353 | SHC-transforming protein 1 | chr1 | GO:0005759 | Not Cancer Driver | No | 84 | 0.144 | 397 | 58 | 0.146 | 0 |
| SHMT2 | SHMT2 | P34897 | Serine hydroxymethyltransferase, mitochondrial | chr12 | GO:0005759 | Not Cancer Driver | No | 57 | 0.113 | 58 | 5 | 0.086 | 1 |
| SIRT3 | SIRT3 | Q9NTG7 | NAD-dependent protein deacetylase sirtuin-3, mitochondrial | chr11 | GO:0005759 | Not Cancer Driver | No | 33 | 0.083 | 60 | 2 | 0.033 | 0 |
| SIRT4 | SIRT4 | Q9Y6E7 | NAD-dependent protein lipoamidase sirtuin-4, mitochondrial | chr12 | GO:0005759 | Not Cancer Driver | No | 46 | 0.146 | 4 | 0 | 0.0 | 0 |
| SIRT5 | SIRT5 | Q9NXA8 | NAD-dependent protein deacylase sirtuin-5, mitochondrial | chr6 | GO:0005759 | Not Cancer Driver | No | 41 | 0.132 | 55 | 7 | 0.127 | 0 |
| SMDT1 | SMDT1 | Q9H4I9 | Essential MCU regulator, mitochondrial | chr22 | GO:0005759 | Not Cancer Driver | No | 6 | 0.056 | 6 | 0 | 0.0 | 0 |
| SOD1 | SOD1 | P00441 | Superoxide dismutase [Cu-Zn] | chr21 | GO:0005759 | Not Cancer Driver | No | 16 | 0.104 | 93 | 9 | 0.097 | 79 |
| SOD2_ENST00000367055 | SOD2 | P04179 | Superoxide dismutase [Mn], mitochondrial | chr6 | GO:0005759 | Not Cancer Driver | No | 32 | 0.144 | 25 | 5 | 0.2 | 0 |
| SSBP1_ENST00000484178 | SSBP1 | Q04837 | Single-stranded DNA-binding protein, mitochondrial | chr7 | GO:0005759 | Not Cancer Driver | No | 27 | 0.182 | 0 | 0 | 0.0 | 6 |
| STYXL1_ENST00000359697 | STYXL1 | Q9Y6J8 | Serine/threonine/tyrosine-interacting-like protein 1 | chr7 | GO:0005759 | Not Cancer Driver | No | 55 | 0.176 | 18 | 3 | 0.167 | 0 |
| SUCLA2 | SUCLA2 | Q9P2R7 | Succinate--CoA ligase [ADP-forming] subunit beta, mitochondrial | chr13 | GO:0005759 | Not Cancer Driver | No | 51 | 0.11 | 46 | 6 | 0.13 | 3 |
| SUCLG1 | SUCLG1 | P53597 | Succinate--CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 48 | 0.139 | 57 | 8 | 0.14 | 3 |
| SUCLG2_ENST00000307227 | SUCLG2 | Q96I99 | Succinate--CoA ligase [GDP-forming] subunit beta, mitochondrial | chr3 | GO:0005759 | Not Cancer Driver | No | 48 | 0.111 | 12 | 2 | 0.167 | 0 |
| SUOX_ENST00000356124 | SUOX | P51687 | Sulfite oxidase, mitochondrial | chr12 | GO:0005759 | Not Cancer Driver | No | 68 | 0.125 | 184 | 32 | 0.174 | 11 |
| SUPV3L1 | SUPV3L1 | Q8IYB8 | ATP-dependent RNA helicase SUPV3L1, mitochondrial | chr10 | GO:0005759 | Not Cancer Driver | No | 72 | 0.092 | 140 | 12 | 0.086 | 0 |
| TARS2 | TARS2 | Q9BW92 | Threonine--tRNA ligase, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 112 | 0.156 | 53 | 10 | 0.189 | 1 |
| TBRG4_ENST00000494076 | TBRG4 | Q969Z0 | FAST kinase domain-containing protein 4 | chr7 | GO:0005759 | Not Cancer Driver | No | 74 | 0.117 | 60 | 2 | 0.033 | 0 |
| TDRD7 | TDRD7 | Q8NHU6 | Tudor domain-containing protein 7 | chr9 | GO:0005759 | Not Cancer Driver | No | 126 | 0.115 | 266 | 38 | 0.143 | 0 |
| TEFM | TEFM | Q96QE5 | Transcription elongation factor, mitochondrial | chr17 | GO:0005759 | Not Cancer Driver | No | 37 | 0.103 | 26 | 5 | 0.192 | 0 |
| TFAM | TFAM | Q00059 | Transcription factor A, mitochondrial | chr10 | GO:0005759 | Not Cancer Driver | No | 25 | 0.102 | 110 | 15 | 0.136 | 1 |
| TFB1M | TFB1M | Q8WVM0 | Dimethyladenosine transferase 1, mitochondrial | chr6 | GO:0005759 | Not Cancer Driver | No | 50 | 0.145 | 26 | 3 | 0.115 | 0 |
| TFB2M | TFB2M | Q9H5Q4 | Dimethyladenosine transferase 2, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 60 | 0.152 | 36 | 6 | 0.167 | 0 |
| THEM4 | THEM4 | Q5T1C6 | Acyl-coenzyme A thioesterase THEM4 | chr1 | GO:0005759 | Not Cancer Driver | No | 19 | 0.079 | 14 | 0 | 0.0 | 0 |
| THEM5 | THEM5 | Q8N1Q8 | Acyl-coenzyme A thioesterase THEM5 | chr1 | GO:0005759 | Not Cancer Driver | No | 39 | 0.158 | 1 | 0 | 0.0 | 0 |
| TIMM44 | TIMM44 | O43615 | Mitochondrial import inner membrane translocase subunit TIM44 | chr19 | GO:0005759 | Not Cancer Driver | No | 56 | 0.124 | 175 | 22 | 0.126 | 0 |
| TK2 | TK2 | O00142 | Thymidine kinase 2, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 23 | 0.087 | 44 | 3 | 0.068 | 11 |
| TMLHE | TMLHE | Q9NVH6 | Trimethyllysine dioxygenase, mitochondrial | chrX | GO:0005759 | Not Cancer Driver | No | 49 | 0.116 | 4 | 0 | 0.0 | 1 |
| TOP3A | TOP3A | Q13472 | DNA topoisomerase 3-alpha | chr17 | GO:0005759 | Not Cancer Driver | No | 103 | 0.103 | 293 | 31 | 0.106 | 2 |
| TP53AIP1 | TP53AIP1 | Q9HCN2 | p53-regulated apoptosis-inducing protein 1 | chr11 | GO:0005759 | Not Cancer Driver | No | 5 | 0.04 | 51 | 3 | 0.059 | 0 |
| TP53_ENST00000445888 | TP53 | P04637 | Cellular tumor antigen p53 | chr17 | GO:0005759 | Census, Compendium | Yes | 2891 | 7.356 | 282 | 1466 | 5.199 | 83 |
| TRAP1 | TRAP1 | Q12931 | Heat shock protein 75 kDa, mitochondrial | chr16 | GO:0005759 | Not Cancer Driver | No | 74 | 0.105 | 110 | 11 | 0.1 | 0 |
| TRIT1 | TRIT1 | Q9H3H1 | tRNA dimethylallyltransferase | chr1 | GO:0005759 | Not Cancer Driver | No | 61 | 0.131 | 121 | 19 | 0.157 | 1 |
| TRMT10C | TRMT10C | Q7L0Y3 | tRNA methyltransferase 10 homolog C | chr3 | GO:0005759 | Not Cancer Driver | No | 56 | 0.139 | 59 | 10 | 0.169 | 2 |
| TRMT5 | TRMT5 | Q32P41 | tRNA (guanine(37)-N1)-methyltransferase | chr14 | GO:0005759 | Not Cancer Driver | No | 46 | 0.09 | 67 | 5 | 0.075 | 2 |
| TRMT61B | TRMT61B | Q9BVS5 | tRNA (adenine(58)-N(1))-methyltransferase, mitochondrial | chr2 | GO:0005759 | Not Cancer Driver | No | 48 | 0.101 | 123 | 10 | 0.081 | 0 |
| TRNT1 | TRNT1 | Q96Q11 | CCA tRNA nucleotidyltransferase 1, mitochondrial | chr3 | GO:0005759 | Not Cancer Driver | No | 60 | 0.138 | 49 | 8 | 0.163 | 7 |
| TRUB2 | TRUB2 | O95900 | Pseudouridylate synthase TRUB2, mitochondrial | chr9 | GO:0005759 | Not Cancer Driver | No | 37 | 0.112 | 73 | 7 | 0.096 | 0 |
| TSFM_ENST00000454289 | TSFM | P43897 | Elongation factor Ts, mitochondrial | chr12 | GO:0005759 | Not Cancer Driver | No | 37 | 0.114 | 74 | 7 | 0.095 | 2 |
| TST_ENST00000249042 | TST | Q16762 | Thiosulfate sulfurtransferase | chr22 | GO:0005759 | Not Cancer Driver | No | 32 | 0.108 | 56 | 6 | 0.107 | 0 |
| TWNK | TWNK | Q96RR1 | Twinkle mtDNA helicase | chr10 | GO:0005759 | Not Cancer Driver | No | 95 | 0.139 | 135 | 11 | 0.081 | 38 |
| TXN2_ENST00000403313 | TXN2 | Q99757 | Thioredoxin, mitochondrial | chr22 | GO:0005759 | Not Cancer Driver | No | 22 | 0.133 | 34 | 4 | 0.118 | 0 |
| TXNRD2 | TXNRD2 | Q9NNW7 | Thioredoxin reductase 2, mitochondrial | chr22 | GO:0005759 | Not Cancer Driver | No | 70 | 0.134 | 46 | 6 | 0.13 | 0 |
| TYMS | TYMS | P04818 | Thymidylate synthase | chr18 | GO:0005759 | Not Cancer Driver | No | 22 | 0.07 | 41 | 0 | 0.0 | 0 |
| UQCC2 | UQCC2 | Q9BRT2 | Ubiquinol-cytochrome-c reductase complex assembly factor 2 | chr6 | GO:0005759 | Not Cancer Driver | No | 10 | 0.079 | 41 | 1 | 0.024 | 0 |
| WARS2 | WARS2 | Q9UGM6 | Tryptophan--tRNA ligase, mitochondrial | chr1 | GO:0005759 | Not Cancer Driver | No | 67 | 0.186 | 31 | 4 | 0.129 | 5 |
| YARS2 | YARS2 | Q9Y2Z4 | Tyrosine--tRNA ligase, mitochondrial | chr12 | GO:0005759 | Not Cancer Driver | No | 59 | 0.124 | 62 | 11 | 0.177 | 2 |